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The fate of medium-chain fatty acids in very long-chain acyl­CoA dehydrogenase deficiency (VLCADD): A matter of sex?
Wehbe, Zeinab; Alatibi, Khaled; Jellusova, Julia; Spiekerkoetter, Ute; Tucci, Sara.
Afiliação
  • Wehbe Z; Laboratory of Clinical Biochemistry and Metabolism, Department of General Pediatrics and Adolescent Medicine, Medical Center-University of Freiburg, Faculty of Medicine, University of Freiburg, Mathildenstrasse 1, Freiburg, Germany; University of Freiburg, Faculty of Biology, Schaenzlestrasse 1, D-7
  • Alatibi K; Laboratory of Clinical Biochemistry and Metabolism, Department of General Pediatrics and Adolescent Medicine, Medical Center-University of Freiburg, Faculty of Medicine, University of Freiburg, Mathildenstrasse 1, Freiburg, Germany; University of Freiburg, Faculty of Biology, Schaenzlestrasse 1, D-7
  • Jellusova J; Department of Molecular Immunology, Institute of Biology III at the Faculty of Biology, Albert-Ludwigs-University of Freiburg, Schänzlestr. 1, 79104 Freiburg, Germany; Signalling Research Centres BIOSS and CIBSS, Albert-Ludwigs-University of Freiburg, Schänzlestr. 18, 79104 Freiburg, Germany.
  • Spiekerkoetter U; Department of General Pediatrics and Adolescent Medicine, Center for Pediatrics and Adolescent Medicine, Medical Center-University of Freiburg, Faculty of Medicine, University of Freiburg, Mathildenstrasse 1, Freiburg, Germany.
  • Tucci S; Laboratory of Clinical Biochemistry and Metabolism, Department of General Pediatrics and Adolescent Medicine, Medical Center-University of Freiburg, Faculty of Medicine, University of Freiburg, Mathildenstrasse 1, Freiburg, Germany. Electronic address: sara.tucci@uniklinik-freiburg.de.
Biochim Biophys Acta Mol Cell Biol Lipids ; 1864(11): 1591-1605, 2019 11.
Article em En | MEDLINE | ID: mdl-31394165

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Doenças Mitocondriais / Acil-CoA Desidrogenase de Cadeia Longa / Ácidos Graxos / Síndrome Congênita de Insuficiência da Medula Óssea / Erros Inatos do Metabolismo Lipídico / Doenças Musculares Tipo de estudo: Prognostic_studies Limite: Animals / Female / Humans / Male Idioma: En Revista: Biochim Biophys Acta Mol Cell Biol Lipids Ano de publicação: 2019 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Doenças Mitocondriais / Acil-CoA Desidrogenase de Cadeia Longa / Ácidos Graxos / Síndrome Congênita de Insuficiência da Medula Óssea / Erros Inatos do Metabolismo Lipídico / Doenças Musculares Tipo de estudo: Prognostic_studies Limite: Animals / Female / Humans / Male Idioma: En Revista: Biochim Biophys Acta Mol Cell Biol Lipids Ano de publicação: 2019 Tipo de documento: Article