Carcinoid Syndrome-Induced Scleroderma-Like Disease.
Dermatopathology (Basel)
; 6(2): 99-104, 2019.
Article
em En
| MEDLINE
| ID: mdl-31700850
ABSTRACT
Scleroderma is a rare complication of carcinoid syndrome and is usually encountered in the setting of a metastatic primary neuroendocrine tumour of the distal ileum. Associated endocardial fibrosis is a frequent finding and the condition carries a poor prognosis. We report a case of scleroderma occurring in a 72-year-old female with metastatic neuroendocrine carcinoma and associated pericardial fibrosis. The use of an alternative nomenclature such as "scleroderma-like" or "sclerodermoid" disease is proposed in order to emphasise its distinction from true idiopathic scleroderma, despite the histopathological similarities on skin biopsy.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Tipo de estudo:
Prognostic_studies
Idioma:
En
Revista:
Dermatopathology (Basel)
Ano de publicação:
2019
Tipo de documento:
Article