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[Hypertrophic cardiomyopathies and ATTR amyloidosis - a current review for clinical practice]. / Hypertrophe Kardiomyopathien und die kardiale ATTR-Amyloidose ­ eine aktuelle Übersicht für den klinischen Alltag.
Tschöpe, Carsten; Elsanhoury, Ahmed; Diekmann, Sonja; Kühl, Uwe.
Afiliação
  • Tschöpe C; Berlin Institute of Health at Charité (BIH), Universitätsmedizin Berlin, BIH Center for Regenerative Therapies (BCRT), Berlin, Germany.
  • Elsanhoury A; Department of Internal Medicine and Cardiology, Charité - Universitätsmedizin Berlin, Campus Virchow-Klinikum, Berlin, Germany.
  • Diekmann S; DZHK (German Centre for Cardiovascular Research), partner site Berlin, Germany.
  • Kühl U; Berlin Institute of Health at Charité (BIH), Universitätsmedizin Berlin, BIH Center for Regenerative Therapies (BCRT), Berlin, Germany.
Dtsch Med Wochenschr ; 147(17): 1127-1134, 2022 09.
Article em De | MEDLINE | ID: mdl-36030786
Cardiomyopathies include dilated and restrictive cardiomyopathies as well as the various forms of hypertrophic cardiomyopathies (HCM). By definition, HCM is considered to occur when left ventricular wall thickness is ≥ 15 mm. This may be masked by genetic sarcomeric diseases, storage diseases, or syndromes. In clinical practice, sarcomere mutations and the cardiac amyloidoses are of particular interest because they are not always easy to distinguish from each other and early diagnosis of the disease is important for prognosis.
Assuntos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Cardiomiopatia Hipertrófica / Amiloidose / Cardiomiopatias Tipo de estudo: Screening_studies Limite: Humans Idioma: De Revista: Dtsch Med Wochenschr Ano de publicação: 2022 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Cardiomiopatia Hipertrófica / Amiloidose / Cardiomiopatias Tipo de estudo: Screening_studies Limite: Humans Idioma: De Revista: Dtsch Med Wochenschr Ano de publicação: 2022 Tipo de documento: Article