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PPAR-gamma agonist pioglitazone recovers mitochondrial quality control in fibroblasts from PITRM1-deficient patients.
Di Donfrancesco, Alessia; Berlingieri, Christian; Giacomello, Marta; Frascarelli, Chiara; Magalhaes Rebelo, Ana Paula; Bindoff, Laurence A; Reeval, Segel; Renbaum, Paul; Santorelli, Filippo M; Massaro, Giulia; Viscomi, Carlo; Zeviani, Massimo; Ghezzi, Daniele; Bottani, Emanuela; Brunetti, Dario.
Afiliação
  • Di Donfrancesco A; Unità di Genetica Medica e Neurogenetica, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy.
  • Berlingieri C; Unità di Genetica Medica e Neurogenetica, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy.
  • Giacomello M; Department of Biology, University of Padova, Padova, Italy.
  • Frascarelli C; Department of Biomedical Sciences, University of Padova, Padova, Italy.
  • Magalhaes Rebelo AP; Unità di Genetica Medica e Neurogenetica, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy.
  • Bindoff LA; Department of Biology, University of Padova, Padova, Italy.
  • Reeval S; Department of Clinical Medicine, University of Bergen, Bergen, Norway.
  • Renbaum P; Shaare Zedek Medical Center, The Hebrew University of Jerusalem, Jerusalem, Israel.
  • Santorelli FM; Shaare Zedek Medical Center, The Hebrew University of Jerusalem, Jerusalem, Israel.
  • Massaro G; Molecular Medicine, IRCCS Fondazione Stella Maris, Calambrone, Italy.
  • Viscomi C; UCL School of Pharmacy, University College London, London, United Kingdom.
  • Zeviani M; Department of Biomedical Sciences, University of Padova, Padova, Italy.
  • Ghezzi D; Department of Neurosciences, University of Padova, Padova, Italy.
  • Bottani E; Unità di Genetica Medica e Neurogenetica, Fondazione IRCCS Istituto Neurologico Carlo Besta, Milan, Italy.
  • Brunetti D; Department of Pathophysiology and Transplantation, University of Milan, Milan, Italy.
Front Pharmacol ; 14: 1220620, 2023.
Article em En | MEDLINE | ID: mdl-37576821

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Front Pharmacol Ano de publicação: 2023 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Front Pharmacol Ano de publicação: 2023 Tipo de documento: Article