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Expert Consensus on the Long-Term Effectiveness of Medical Nutrition Therapy and Its Impact on the Outcomes of Adults with Phenylketonuria.
Rocha, Júlio César; Ahring, Kirsten K; Bausell, Heather; Bilder, Deborah A; Harding, Cary O; Inwood, Anita; Longo, Nicola; Muntau, Ania C; Pessoa, André L Santos; Rohr, Fran; Sivri, Serap; Hermida, Álvaro.
Afiliação
  • Rocha JC; NOVA Medical School, Faculdade de Ciências Médicas, Universidade NOVA de Lisboa, Campo Mártires da Pátria 130, 1169-056 Lisboa, Portugal.
  • Ahring KK; Reference Centre of Inherited Metabolic Diseases, Centro Hospitalar Universitário de Lisboa Central, Rua Jacinta Marto, 1169-045 Lisboa, Portugal.
  • Bausell H; CINTESIS@RISE, Nutrition and Metabolism, NOVA Medical School, Faculdade de Ciências Médicas, NMS, FCM, Universidade NOVA de Lisboa, Campo Mártires da Pátria 130, 1169-056 Lisboa, Portugal.
  • Bilder DA; Departments of Paediatrics and Clinical Genetics, PKU Clinic, Copenhagen University Hospital, Rigshospitalet, Blegdamsvej 9, 2100 Copenhagen, Denmark.
  • Harding CO; Division of Genetics, Genomics, and Metabolism, Ann & Robert H Lurie Children's Hospital of Chicago, 225 E. Chicago Ave., Chicago, IL 60611, USA.
  • Inwood A; Department of Psychiatry, Division of Child & Adolescent Psychiatry, University of Utah Huntsman Mental Health Institute, 501 Chipeta Way, Salt Lake City, UT 84108, USA.
  • Longo N; Department of Molecular and Medical Genetics, Oregon Health & Science University, 3222 SW Research Drive, Portland, OR 97239, USA.
  • Muntau AC; Queensland Lifespan Metabolic Medicine Service, Queensland Children's Hospital, 501 Stanley St., South Brisbane, QLD 4101, Australia.
  • Pessoa ALS; School of Nursing and Social Work, The University of Queensland, Chamberlain Building, St. Lucia, QLD 4072, Australia.
  • Rohr F; Department of Pediatrics, Division of Medical Genetics, University of Utah School of Medicine, 295 Chipeta Way, Salt Lake City, UT 84108, USA.
  • Sivri S; Department of Pediatrics, University Children's Hospital, University Medical Centre Hamburg-Eppendorf, Martinistraße 52, 20246 Hamburg, Germany.
  • Hermida Á; Albert Sabin Children's Hospital, R. Tertuliano Sales, 544-Vila União, Fortaleza 60410-794, CE, Brazil.
Nutrients ; 15(18)2023 Sep 11.
Article em En | MEDLINE | ID: mdl-37764724

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Fenilcetonúrias / Terapia Nutricional Tipo de estudo: Guideline Limite: Adult / Child / Humans / Newborn Idioma: En Revista: Nutrients Ano de publicação: 2023 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Fenilcetonúrias / Terapia Nutricional Tipo de estudo: Guideline Limite: Adult / Child / Humans / Newborn Idioma: En Revista: Nutrients Ano de publicação: 2023 Tipo de documento: Article