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A rare inflammatory myofibroblastic tumor appearing both inside and outside the heart.
Li, Jiarong; Liu, Jijia; Yao, Xingwang; Yang, Jinfu.
Afiliação
  • Li J; Department of Cardiovascular Surgery, The Second Xiangya Hospital, Central South University, Middle Renmin Road 139, Changsha, 410011, China.
  • Liu J; Department of Cardiovascular Surgery, The Second Xiangya Hospital, Central South University, Middle Renmin Road 139, Changsha, 410011, China.
  • Yao X; Clinical Nursing Teaching and Research Section, The Second Xiangya Hospital, Central South University, Changsha, 410011, China. 739479210@qq.com.
  • Yang J; Department of Cardiovascular Surgery, The Second Xiangya Hospital, Central South University, Middle Renmin Road 139, Changsha, 410011, China. yjf19682005@csu.edu.cn.
Eur J Med Res ; 29(1): 132, 2024 Feb 17.
Article em En | MEDLINE | ID: mdl-38368344
ABSTRACT

BACKGROUND:

Inflammatory myofibroblastic tumor (IMT) is an uncommon cardiac tumor that primarily affects infants, children, and young adults. While complete surgical resection generally leads to a favorable prognosis, accurate diagnostic tests remain limited. CASE PRESENTATION We describe the case of a 26-year-old female who had a dual tumor inside and outside the heart and was misdiagnosed by echocardiography and MRI. We also review 71 cases of cardiac IMTs from the literature regarding their epidemiology, clinical presentation, and outcome.

CONCLUSION:

Early detection of this rare disorder is essential for optimal surgical management.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Granuloma de Células Plasmáticas / Neoplasias Cardíacas Limite: Adult / Child / Female / Humans / Infant Idioma: En Revista: Eur J Med Res Ano de publicação: 2024 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Granuloma de Células Plasmáticas / Neoplasias Cardíacas Limite: Adult / Child / Female / Humans / Infant Idioma: En Revista: Eur J Med Res Ano de publicação: 2024 Tipo de documento: Article