1.
J Pediatr
; 161(5): 950-3, 2012 Nov.
Artigo
em Inglês
| MEDLINE
| ID: mdl-22809661
RESUMO
DiGeorge syndrome is associated with a T-lymphocyte immunodeficiency. The prevalence of hypogammaglobulinemia has not been reported. We found that 3% of patients with DiGeorge syndrome were receiving immunoglobulin replacement therapy and 6% of patients over the age of 3 years had hypogammaglobulinemia. We conclude that DiGeorge syndrome is associated with significant humoral immune deficiency.