[Mediastinal bronchial artery aneurysm: treatment with stent-graft]. / Anévrisme médiastinal de l'artère bronchique : traitement par endoprothèse aortique.

Mediastinal bronchial artery aneurysm is rare but potentially life-threatening, and requires prompt treatment to avert rupture with catastrophic results. Inflammatory conditions dominate the aetiologies. Conventional therapies are surgery via thoracotomy and endovascular embolization. We report a case of a giant saccular aneurysm of the bronchial artery described in an 80-year-old man, adjacent to the descending aorta, simulating aortic aneurysm and causing esophageal compression. It was totally excluded with an aortic stent-graft (TX2, Cook) performed through femoral access. Our case is the fourth reported of mediastinal bronchial aneurysm stent-graft exclusion. The analysis of success, complications rate and hospital stay duration favors endovascular grafting comparing with conventional techniques.

[Involvement of peripheral arteries in Von Recklinghausen neurofibromatosis]. / L'atteinte des artères périphériques au cours de la neurofibromatose de Von Recklinghausen. Étude de deux cas.

Arterial lesions are relatively rare in neurofibromatosis type I but can have potentially serious consequences for the patient. We report two clinical cases of peripheral arterial involvement in neurofibromatosis type 1. The first case was a 25-year-old female with Von Recklinghausen disease who developed a swollen tender mass around her left arm. The arterial CT scan revealed a false aneurysm of the brachial artery. The surgical procedure involved repair of the false aneurysm, and ligation of the brachial artery. Intra- and postoperative bleeding was severe, leading to hemodynamic instability and impaired hemostasis. The patient died on day 2, postoperatively. The second case involved a 17-year-old male with Von Recklinghausen disease who presented stage II arteritis of the right lower limb. Arteriography revealed a long stenosis of the right superficial femoral artery extending to the popliteal artery and an important collateral circulation in the leg arteries. Medical treatment with regular clinical supervision was recommended in this patient.

[Left atrial myxoma: a rare cause of acute occlusion of the aorta. Case report and review of the literature]. / Myxome de l'oreillette gauche : une cause rare d'occlusion aiguë de l'aorte. A propos d'un cas et revue de la littérature.

We present an observation of a 42-year-old patient admitted in urgency for lower limbs weakness followed by paralysis. At physical examination the lower limbs were cold. Pulses of the lower limbs could not be palpated. Color Duplex ultrasonography revealing an embolus occluding both the infrarenal aorta and bilateral iliac arteries. The aortoiliac embolus was removed by balloon endarterectomy through the femoral arteries with evacuation of a transparent, gelatinous embolus followed by extensive fasciotomies. Two-dimensional echocardiography showed a mass in the left atrium. Pathological examination of the material embolic confirmed the diagnosis of the cardiac myxoma. The clinical course was marked by the development of a syndrome of revascularization; death occurred the fourth day of hospitalization. This case highlights the need for pre- and perioperative measures to be taken to overcome hyperkalemia and acute renal failure when revascularizing acute, massive, prolonged ischemia of the lower body.

[Vascular type of Ehlers-Danlos syndrome: a rare cause of spontaneous pseudo-aneurysms]. / Syndrome d'Ehlers-Danlos de type vasculaire : une cause rare de faux-anévrismes artériels spontanés.

We report a case of a 20-year-old-man who was admitted to our hospital through the emergency room for a swelling of the right thigh, which had appeared spontaneously without fever. The physical exam was highly suggestive of a vascular mass. The arterial CT scan of the right lower limb revealed a pseudo-aneurysm of a branch of the deep right femoral artery. The diagnosis of vascular type of Ehlers Danlos syndrome was established on clinical criteria. The successful management was surgical by the excision of the pseudoaneurysm and the ligation of the feeding branch that supplied the pseudoaneurysm. The postsurgical follow-up was uneventful and the clinical course was smooth with no further complications.

[Coeliac trunk aneurysm revealing Behçet disease (2 case reports)]. / Anévrisme du tronc coeliaque révélant la maladie de Behçet. A propos de deux cas.

The Behçet's disease is a vasculitis of an unknown origin. Vascular inflammatory lesions predominantly affect veins, potentially leading to superficial or deep thrombophlebitis. Arterial involvement is rare, mainly aneurysms. We display two case reports of patients where Behçet's disease is revealed by celiac trunk aneurysm. The symptoms are nonspecific. Ultrasound Doppler and angioscan are a key to the diagnosis. The two patients received medical and surgical treatment. By these two case reports, we insist that the diagnosis of Behçet's disease should be evoqued in any young patient with arterial aneurysm.