Detalhe da pesquisa
1.
Improvement in Lung Clearance Index and Chest Computed Tomography Scores with Elexacaftor/Tezacaftor/Ivacaftor Treatment in People with Cystic Fibrosis Aged 12 Years and Older - The RECOVER Trial.
Am J Respir Crit Care Med
; 208(9): 917-929, 2023 11 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-37703083
2.
The clinical impact of Lumacaftor-Ivacaftor on structural lung disease and lung function in children aged 6-11 with cystic fibrosis in a real-world setting.
Respir Res
; 24(1): 199, 2023 Aug 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-37568199
3.
Precise Targeting of miRNA Sites Restores CFTR Activity in CF Bronchial Epithelial Cells.
Mol Ther
; 28(4): 1190-1199, 2020 04 08.
Artigo
em Inglês
| MEDLINE | ID: mdl-32059764
4.
A short-term evaluation of a prototype disposable Oscillating Positive Expiratory Pressure (OPEP) device in a cohort of children with cystic fibrosis.
BMC Pulm Med
; 21(1): 158, 2021 May 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-33980186
5.
An initial evaluation of the safety of a disposable oscillating positive expiratory pressure device in patients with chronic obstructive pulmonary disease: a sort-term pilot study.
BMC Pulm Med
; 21(1): 326, 2021 Oct 19.
Artigo
em Inglês
| MEDLINE | ID: mdl-34666748
6.
Increased extracellular vesicles mediate inflammatory signalling in cystic fibrosis.
Thorax
; 75(6): 449-458, 2020 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-32265339
7.
Repeatability of transient elastography in children.
Pediatr Res
; 88(4): 587-592, 2020 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-32357363
8.
Cystic Fibrosis Diagnosis in Newborns, Children, and Adults.
Semin Respir Crit Care Med
; 40(6): 701-714, 2019 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-31679154
9.
Detection of Neisseria meningitidis in a paediatric patient with septic arthritis using multiplexed diagnostic PCR targeting meningitis/encephalitis (ME).
Ann Clin Microbiol Antimicrob
; 17(1): 14, 2018 Mar 23.
Artigo
em Inglês
| MEDLINE | ID: mdl-29571294
10.
Ivacaftor and Airway Inflammation in Preschool Children with Cystic Fibrosis.
Am J Respir Crit Care Med
; 204(5): 605-608, 2021 09 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-34077699
11.
Lower Airway Infection in Preschool Children with Cystic Fibrosis: An International Comparison.
Am J Respir Crit Care Med
; 201(6): 748-750, 2020 03 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-31769996
12.
The first reported case of Burkholderia contaminans in patients with cystic fibrosis in Ireland: from the Sargasso Sea to Irish Children.
BMC Pulm Med
; 16(1): 57, 2016 Apr 22.
Artigo
em Inglês
| MEDLINE | ID: mdl-27103163
13.
Acinetobacter baumannii Infection in a Child with Cystic Fibrosis.
J Paediatr Child Health
; 57(7): 1148-1149, 2021 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-33929764
14.
A case of failed eradication of cystic fibrosis-related sinus colonisation by Pseudomonas aeruginosa.
BMC Pulm Med
; 15: 114, 2015 Oct 06.
Artigo
em Inglês
| MEDLINE | ID: mdl-26445233
15.
Eight-month-old girl with feeding difficulties and an enlarged liver.
Arch Dis Child Educ Pract Ed
; 105(6): 369-371, 2020 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-31073036
16.
Reduced 15-lipoxygenase 2 and lipoxin A4/leukotriene B4 ratio in children with cystic fibrosis.
Eur Respir J
; 44(2): 394-404, 2014 Aug.
Artigo
em Inglês
| MEDLINE | ID: mdl-24696116
17.
Design and initial testing of a novel disposable oscillating positive expiratory pressure device.
Ir J Med Sci
; 192(5): 2291-2299, 2023 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-36417107
18.
Indwelling central venous catheter infection with Chryseobacterium shandongense - successful eradication in a 5-year-old with cystic fibrosis.
Access Microbiol
; 5(12)2023.
Artigo
em Inglês
| MEDLINE | ID: mdl-38188240
19.
European survey of newborn bloodspot screening for CF: opportunity to address challenges and improve performance.
J Cyst Fibros
; 22(3): 484-495, 2023 May.
Artigo
em Inglês
| MEDLINE | ID: mdl-36372700
20.
Reduction in abdominal symptoms (CFAbd-Score), faecal M2-pyruvate-kinase and Calprotectin over one year of treatment with Elexacaftor-Tezacaftor-Ivacaftor in people with CF aged ≥12 years - The RECOVER study.
J Cyst Fibros
; 2023 Oct 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-37806792