Detalhe da pesquisa
1.
MTO1 mediates tissue specificity of OXPHOS defects via tRNA modification and translation optimization, which can be bypassed by dietary intervention.
Hum Mol Genet
; 24(8): 2247-66, 2015 Apr 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-25552653
2.
Hodgkin and Reed-Sternberg cells of classical Hodgkin lymphoma are highly dependent on oxidative phosphorylation.
Int J Cancer
; 138(9): 2231-46, 2016 May 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-26595876
3.
Defining the action spectrum of potential PGC-1α activators on a mitochondrial and cellular level in vivo.
Hum Mol Genet
; 23(9): 2400-15, 2014 May 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-24334768
4.
Partial complex I deficiency due to the CNS conditional ablation of Ndufa5 results in a mild chronic encephalopathy but no increase in oxidative damage.
Hum Mol Genet
; 23(6): 1399-412, 2014 Mar 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-24154540
5.
Mitochondrial protein acetylation mediates nutrient sensing of mitochondrial protein synthesis and mitonuclear protein balance.
IUBMB Life
; 66(11): 793-802, 2014 Nov.
Artigo
em Inglês
| MEDLINE | ID: mdl-25400169
6.
Leptin is involved in age-dependent changes in response to systemic inflammation in the rat.
Brain Behav Immun
; 36: 128-38, 2014 Feb.
Artigo
em Inglês
| MEDLINE | ID: mdl-24513873
7.
Mitochondrial myopathy induces a starvation-like response.
Hum Mol Genet
; 19(20): 3948-58, 2010 Oct 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-20656789
8.
Increased muscle PGC-1alpha expression protects from sarcopenia and metabolic disease during aging.
Proc Natl Acad Sci U S A
; 106(48): 20405-10, 2009 Dec 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-19918075
9.
A metabolic shift induced by a PPAR panagonist markedly reduces the effects of pathogenic mitochondrial tRNA mutations.
J Cell Mol Med
; 15(11): 2317-25, 2011 Nov.
Artigo
em Inglês
| MEDLINE | ID: mdl-21129152
10.
Monitoring the redox and protonation dependent contributions of cardiolipin in electrochemically induced FTIR difference spectra of the cytochrome bc(1) complex from yeast.
Biochim Biophys Acta
; 1787(6): 617-25, 2009 Jun.
Artigo
em Inglês
| MEDLINE | ID: mdl-19413949
11.
Role of phospholipids in respiratory cytochrome bc(1) complex catalysis and supercomplex formation.
Biochim Biophys Acta
; 1787(6): 609-16, 2009 Jun.
Artigo
em Inglês
| MEDLINE | ID: mdl-19254687
12.
PGC-1alpha activation as a therapeutic approach in mitochondrial disease.
IUBMB Life
; 61(11): 1051-62, 2009 Nov.
Artigo
em Inglês
| MEDLINE | ID: mdl-19859975
13.
Endurance exercise is protective for mice with mitochondrial myopathy.
J Appl Physiol (1985)
; 106(5): 1712-9, 2009 May.
Artigo
em Inglês
| MEDLINE | ID: mdl-19286571
14.
Translation and Assembly of Radiolabeled Mitochondrial DNA-Encoded Protein Subunits from Cultured Cells and Isolated Mitochondria.
Methods Mol Biol
; 1351: 115-29, 2016.
Artigo
em Inglês
| MEDLINE | ID: mdl-26530678
15.
Keep the fire burning: Current avenues in the quest of treating mitochondrial disorders.
Mitochondrion
; 24: 32-49, 2015 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-26134435
16.
Long-term survival in a child with severe encephalopathy, multiple respiratory chain deficiency and GFM1 mutations.
Front Genet
; 6: 102, 2015.
Artigo
em Inglês
| MEDLINE | ID: mdl-25852744
17.
Corrigendum: Long-term survival in a child with severe encephalopathy, multiple respiratory chain deficiency and GFM1 mutations.
Front Genet
; 6: 254, 2015.
Artigo
em Inglês
| MEDLINE | ID: mdl-26284110
18.
Post-translational modification of mitochondria as a novel mode of regulation.
Exp Gerontol
; 56: 202-20, 2014 Aug.
Artigo
em Inglês
| MEDLINE | ID: mdl-24632076
19.
Glucose substitution prolongs maintenance of energy homeostasis and lifespan of telomere dysfunctional mice.
Nat Commun
; 5: 4924, 2014 Sep 18.
Artigo
em Inglês
| MEDLINE | ID: mdl-25233189
20.
MTO1-deficient mouse model mirrors the human phenotype showing complex I defect and cardiomyopathy.
PLoS One
; 9(12): e114918, 2014.
Artigo
em Inglês
| MEDLINE | ID: mdl-25506927