A recently recognised chronic inflammatory disease of early onset characterised by the triad of rash, central nervous system involvement and arthropathy.
Clin Exp Rheumatol
; 19(1): 103-6, 2001.
Article
em En
| MEDLINE
| ID: mdl-11247311
ABSTRACT
Chronic Infantile Neurological Cutaneous and Articular (CINCA) syndrome, also called Neonatal Onset Multisystemic Inflammatory Disease (NOMID) is characterised by the triad of cutaneous rash, chronic meningitis and arthropathy. It is a chronic inflammatory illness that starts most often at birth and persists for the whole lifespan of the patient. Attempts at therapy have been disappointing. The long-term prognosis is poor, with progressive deafness and visual impairment, and worsening of the central nervous system manifestations. Some cases of death have been reported secondary to infection, vasculitis and amyloidosis. Usually observed as sporadic cases, some familial association is recognised.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Artropatia Neurogênica
/
Exantema
/
Inflamação
Tipo de estudo:
Prognostic_studies
Limite:
Humans
/
Infant
/
Newborn
Idioma:
En
Revista:
Clin Exp Rheumatol
Ano de publicação:
2001
Tipo de documento:
Article
País de afiliação:
França