Maffucci's syndrome complicated by intracranial chondrosarcoma: two new illustrative cases.
Arq Neuropsiquiatr
; 65(3B): 816-21, 2007 Sep.
Article
em En
| MEDLINE
| ID: mdl-17952287
ABSTRACT
Maffucci's syndrome is a rare congenital condition, sometimes misdiagnosed as Ollier's disease, characterized by multiple enchondromas combined with hemangiomas and phlebectasia. Coexisting primary malignancies have been described sporadically. We report two cases of Maffucci's syndrome associated with cranial base chondrosarcoma, emphasizing pathophysiological features and the challenging management of intracranial chondrosarcomas. To the best of our knowledge, only twelve similar cases have been reported in the literature.
Buscar no Google
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Condrossarcoma
/
Neoplasias da Base do Crânio
/
Encondromatose
Tipo de estudo:
Diagnostic_studies
Limite:
Adult
/
Humans
/
Male
Idioma:
En
Revista:
Arq Neuropsiquiatr
Ano de publicação:
2007
Tipo de documento:
Article
País de afiliação:
Brasil