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Ivacaftor in a young boy with the rare gating mutation S549R--use of lung clearance index to track progress: a case report.
Lenherr, Nina; Lurà, Marco; Trachsel, Daniel; Latzin, Philipp; Hammer, Juerg.
Afiliação
  • Lenherr N; Division of Intensive Care and Pulmonology, University Children's Hospital Basel (UKBB), University of Basel, Spitalstrasse 33, CH-4056, Basel, Switzerland. nina.lenherr@ukbb.ch.
  • Lurà M; Division of Intensive Care and Pulmonology, University Children's Hospital Basel (UKBB), University of Basel, Spitalstrasse 33, CH-4056, Basel, Switzerland. marco.lura@ukbb.ch.
  • Trachsel D; Division of Intensive Care and Pulmonology, University Children's Hospital Basel (UKBB), University of Basel, Spitalstrasse 33, CH-4056, Basel, Switzerland. daniel.trachsel@ukbb.ch.
  • Latzin P; Division of Intensive Care and Pulmonology, University Children's Hospital Basel (UKBB), University of Basel, Spitalstrasse 33, CH-4056, Basel, Switzerland. philipp.latzin@ukbb.ch.
  • Hammer J; Division of Intensive Care and Pulmonology, University Children's Hospital Basel (UKBB), University of Basel, Spitalstrasse 33, CH-4056, Basel, Switzerland. juerg.hammer@ukbb.ch.
BMC Pulm Med ; 15: 123, 2015 Oct 16.
Article em En | MEDLINE | ID: mdl-26474553

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Quinolonas / Regulador de Condutância Transmembrana em Fibrose Cística / Fibrose Cística / Aminofenóis Limite: Child / Humans / Male Idioma: En Revista: BMC Pulm Med Ano de publicação: 2015 Tipo de documento: Article País de afiliação: Suíça

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Quinolonas / Regulador de Condutância Transmembrana em Fibrose Cística / Fibrose Cística / Aminofenóis Limite: Child / Humans / Male Idioma: En Revista: BMC Pulm Med Ano de publicação: 2015 Tipo de documento: Article País de afiliação: Suíça