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In vivo monitoring of urea cycle activity with (13)C-acetate as a tracer of ureagenesis.
Opladen, Thomas; Lindner, Martin; Das, Anibh M; Marquardt, Thorsten; Khan, Aneal; Emre, Sukru H; Burton, Barbara K; Barshop, Bruce A; Böhm, Thea; Meyburg, Jochen; Zangerl, Kathrin; Mayorandan, Sebene; Burgard, Peter; Dürr, Ulrich H N; Rosenkranz, Bernd; Rennecke, Jörg; Derbinski, Jens; Yudkoff, Marc; Hoffmann, Georg F.
Afiliação
  • Opladen T; Division of Neuropediatrics and Pediatric Metabolic Medicine, University Children's Hospital Heidelberg, Germany. Electronic address: Thomas.Opladen@med.uni-heidelberg.de.
  • Lindner M; Division of Neuropediatrics and Pediatric Metabolic Medicine, University Children's Hospital Heidelberg, Germany; Division of Neuropaediatrics, Prevention, Endocrinology and Pediatric Metabolic Diseases, University Children's Hospital Frankfurt, Germany. Electronic address: Martin.Lindner@kgu.de.
  • Das AM; Division of Metabolic Disorders, Medical School Hannover, Germany. Electronic address: Das.Anibh@mh-hannover.de.
  • Marquardt T; Division of Metabolic Disorders, University Children's Hospital Münster, Germany. Electronic address: Thorsten.Marquardt@ukmuenster.de.
  • Khan A; Department of Medical Genetics & Pediatrics, Alberta Children's Hospital, Calgary, Canada. Electronic address: khaa@ucalgary.ca.
  • Emre SH; Department of Surgery, Yale University School of Medicine, New Haven, USA. Electronic address: sukru.emre@yale.edu.
  • Burton BK; Children's Memorial Hospital, Chicago, USA. Electronic address: BBurton@luriechildrens.org.
  • Barshop BA; Department of Pediatrics, University of California, San Diego, La Jolla, CA, USA. Electronic address: bbarshop@ucsd.edu.
  • Böhm T; Cytonet GmbH & Co. KG, Albert-Ludwig-Grimm-Str. 20, Weinheim, Germany. Electronic address: Thea.boehm@gmx.net.
  • Meyburg J; Division of Neuropediatrics and Pediatric Metabolic Medicine, University Children's Hospital Heidelberg, Germany. Electronic address: Jochen.Meyburg@med.uni-heidelberg.de.
  • Zangerl K; Division of Neuropediatrics and Pediatric Metabolic Medicine, University Children's Hospital Heidelberg, Germany. Electronic address: kathrin.zangerl@gmail.com.
  • Mayorandan S; Division of Metabolic Disorders, Medical School Hannover, Germany. Electronic address: Sebene.Mayorandan@ukmuenster.de.
  • Burgard P; Division of Neuropediatrics and Pediatric Metabolic Medicine, University Children's Hospital Heidelberg, Germany. Electronic address: Peter.Burgard@med.uni-heidelberg.de.
  • Dürr UH; Cytonet GmbH & Co. KG, Albert-Ludwig-Grimm-Str. 20, Weinheim, Germany. Electronic address: Ulrich.Duerr@cytonet.de.
  • Rosenkranz B; Division of Clinical Pharmacology, Faculty of Medicine and Health Sciences, Department of Medicine, Stellenbosch University, South Africa. Electronic address: rosenkranz@sun.ac.za.
  • Rennecke J; Cytonet GmbH & Co. KG, Albert-Ludwig-Grimm-Str. 20, Weinheim, Germany. Electronic address: Joerg.Rennecke@cytonet.de.
  • Derbinski J; Cytonet GmbH & Co. KG, Albert-Ludwig-Grimm-Str. 20, Weinheim, Germany. Electronic address: Jens.Derbinski@cytonet.de.
  • Yudkoff M; Division of Metabolic Disease, Children's Hospital of Philadelphia, USA. Electronic address: yudkoff@email.chop.edu.
  • Hoffmann GF; Division of Neuropediatrics and Pediatric Metabolic Medicine, University Children's Hospital Heidelberg, Germany. Electronic address: Georg.Hoffmann@med.uni-heidelberg.de.
Mol Genet Metab ; 117(1): 19-26, 2016 Jan.
Article em En | MEDLINE | ID: mdl-26597322

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Ureia / Acetato de Sódio / Distúrbios Congênitos do Ciclo da Ureia Tipo de estudo: Diagnostic_studies / Evaluation_studies / Prognostic_studies Limite: Adolescent / Adult / Child / Child, preschool / Female / Humans / Infant / Male / Middle aged / Newborn Idioma: En Revista: Mol Genet Metab Assunto da revista: BIOLOGIA MOLECULAR / BIOQUIMICA / METABOLISMO Ano de publicação: 2016 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Ureia / Acetato de Sódio / Distúrbios Congênitos do Ciclo da Ureia Tipo de estudo: Diagnostic_studies / Evaluation_studies / Prognostic_studies Limite: Adolescent / Adult / Child / Child, preschool / Female / Humans / Infant / Male / Middle aged / Newborn Idioma: En Revista: Mol Genet Metab Assunto da revista: BIOLOGIA MOLECULAR / BIOQUIMICA / METABOLISMO Ano de publicação: 2016 Tipo de documento: Article