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Lipid-induced endoplasmic reticulum stress in X-linked adrenoleukodystrophy.
van de Beek, Malu-Clair; Ofman, Rob; Dijkstra, Inge; Wijburg, Frits; Engelen, Marc; Wanders, Ronald; Kemp, Stephan.
Afiliação
  • van de Beek MC; Department of Clinical Chemistry, Laboratory Genetic Metabolic Diseases, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands.
  • Ofman R; Department of Clinical Chemistry, Laboratory Genetic Metabolic Diseases, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands.
  • Dijkstra I; Department of Clinical Chemistry, Laboratory Genetic Metabolic Diseases, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands.
  • Wijburg F; Department of Pediatrics, Emma Children's Hospital, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands.
  • Engelen M; Department of Pediatrics, Emma Children's Hospital, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands.
  • Wanders R; Department of Clinical Chemistry, Laboratory Genetic Metabolic Diseases, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands; Department of Pediatrics, Emma Children's Hospital, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands.
  • Kemp S; Department of Clinical Chemistry, Laboratory Genetic Metabolic Diseases, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands; Department of Pediatrics, Emma Children's Hospital, Academic Medical Center, University of Amsterdam, Amsterdam, The Netherlands. Electronic address:
Biochim Biophys Acta Mol Basis Dis ; 1863(9): 2255-2265, 2017 09.
Article em En | MEDLINE | ID: mdl-28666219

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Estresse Oxidativo / Adrenoleucodistrofia / Ácidos Graxos / Fibroblastos / Mitocôndrias Limite: Humans / Male Idioma: En Revista: Biochim Biophys Acta Mol Basis Dis Ano de publicação: 2017 Tipo de documento: Article País de afiliação: Holanda

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Estresse Oxidativo / Adrenoleucodistrofia / Ácidos Graxos / Fibroblastos / Mitocôndrias Limite: Humans / Male Idioma: En Revista: Biochim Biophys Acta Mol Basis Dis Ano de publicação: 2017 Tipo de documento: Article País de afiliação: Holanda