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TAFRO syndrome complicated by porto-sinusoidal vascular liver disease with portal hypertension: a case report.
Hayashi, Manabu; Wada, Jun; Fujita, Masashi; Asano, Tomoyuki; Matsuoka, Naoki; Fujita, Yuya; Temmoku, Jumpei; Matsumoto, Haruki; Yashio-Furuya, Makiko; Sato, Shuzo; Kobayashi, Hiroko; Watanabe, Hiroshi; Ryoichiro, Kobashi; Waragai, Yuichi; Suzuki, Erina; Kiko, Yuichiro; Abe, Kazumichi; Takahashi, Atsushi; Masuda, Tomoyuki; Hashimoto, Yuko; Migita, Kiyoshi; Ohira, Hiromasa.
Afiliação
  • Hayashi M; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan. m884884@fmu.ac.jp.
  • Wada J; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Fujita M; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Asano T; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Matsuoka N; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Fujita Y; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Temmoku J; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Matsumoto H; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Yashio-Furuya M; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Sato S; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Kobayashi H; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Watanabe H; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Ryoichiro K; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Waragai Y; Department of Gastroenterology, Soma General Hospital, Soma, Japan.
  • Suzuki E; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Kiko Y; Department of Gastroenterology, Soma General Hospital, Soma, Japan.
  • Abe K; Department of Diagnostic Pathology, Fukushima Medical University, Fukushima, Japan.
  • Takahashi A; Department of Diagnostic Pathology, Fukushima Medical University, Fukushima, Japan.
  • Masuda T; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Hashimoto Y; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Migita K; Department of Pathology, School of Medicine, Iwate Medical University, Iwate, Japan.
  • Ohira H; Department of Diagnostic Pathology, Fukushima Medical University, Fukushima, Japan.
Clin J Gastroenterol ; 14(6): 1711-1717, 2021 Dec.
Article em En | MEDLINE | ID: mdl-34487333
ABSTRACT
Porto-sinusoidal vascular liver disease (PSVD) is a disorder that can cause portal hypertension without liver cirrhosis. TAFRO syndrome is a systemic inflammatory disorder with a background of immunological abnormalities. We report a case of TAFRO syndrome complicated by PSVD with portal hypertension. A 39-year-old man developed refractory ascites and esophageal varices. Lymph node histology revealed multicentric Castleman disease-like features. Intravenous methylprednisolone and tocilizumab therapy improved ascites and renal dysfunction, but the patient developed severe infections. The diagnosis of TAFRO syndrome in patients complicated by PSVD with portal hypertension encourages the consideration of appropriate treatment for these patients.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Doenças Vasculares / Hiperplasia do Linfonodo Gigante / Hipertensão Portal Limite: Adult / Humans / Male Idioma: En Revista: Clin J Gastroenterol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Japão
Texto completo
Imprimir
XML
PubMed Links
Buscar no Google

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Doenças Vasculares / Hiperplasia do Linfonodo Gigante / Hipertensão Portal Limite: Adult / Humans / Male Idioma: En Revista: Clin J Gastroenterol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Japão