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Sustained effectiveness of elexacaftor-tezacaftor-ivacaftor in lung transplant candidates with cystic fibrosis.
Martin, Clémence; Reynaud-Gaubert, Martine; Hamidfar, Rebecca; Durieu, Isabelle; Murris-Espin, Marlène; Danner-Boucher, Isabelle; Chiron, Raphaël; Leroy, Sylvie; Douvry, Benoit; Grenet, Dominique; Mely, Laurent; Ramel, Sophie; Montcouquiol, Sylvie; Lemonnier, Lydie; Burnet, Espérie; Paillasseur, Jean-Louis; Da Silva, Jennifer; Burgel, Pierre-Régis.
Afiliação
  • Martin C; Université de Paris, Institut Cochin, Inserm U1016, Paris, France; Respiratory Medicine and Cystic Fibrosis National Reference Center, Cochin Hospital, Assistance Publique Hôpitaux de Paris (AP-HP), Paris, France; ERN-Lung CF network, Frankfurt, Germany.
  • Reynaud-Gaubert M; Department of Respiratory Medicine and Lung Transplantation, Adult Cystic Fibrosis Center Aix Marseille Université, APHM, Hôpital Nord, Marseille, France.
  • Hamidfar R; Service Hospitalo-Universitaire de Pneumologie et Physiologie, Pôle Thorax et Vaisseaux, Centre Hospitalier Universitaire de Grenoble-Alpes, La Tronche, France.
  • Durieu I; Centre de référence Adulte de la Mucoviscidose, Service de médecine interne, Hospices Civils de Lyon, Pierre Bénite, France; Université de Lyon, Équipe d'Accueil Health Services and Performance Research (HESPER) 7425, Lyon, France.
  • Murris-Espin M; Cystic Fibrosis Center Service de Pneumologie Pôle des Voies Respiratoires, Hôpital Larrey CHU de Toulouse, Toulouse, France.
  • Danner-Boucher I; Service de Pneumologie, L'Institut Du Thorax, CHU Nantes, Nantes, France.
  • Chiron R; Cystic Fibrosis Center, Hôpital Arnaud de Villeneuve, Centre Hospitalier Universitaire de Montpellier, Montpellier, France.
  • Leroy S; Pulmonology Department, Université Côte d'Azur, Centre Hospitalier Universitaire de Nice, Fédération Hospitalo-Universitaire OncoAge, CNRS, Inserm, Institute for Research on Cancer and Aging Nice Team 3, Nice, France.
  • Douvry B; Service de Pneumologie, Centre Hospitalier Intercommunal, FHU SENEC, Créteil, France.
  • Grenet D; CRCM - Centre de Transplantation Pulmonaire, Service de pneumologie, Hôpital Foch, Suresnes, France.
  • Mely L; Hôpital Renée Sabran, Cystic Fibrosis Center, Giens, France.
  • Ramel S; Centre de Ressources et de Compétences de la Mucoviscidose, Fondation Ildys, Roscoff, France.
  • Montcouquiol S; CHU Clermont-Ferrand, Centre de Référence et de Compétence Mucoviscidose, Clermont-Ferrand, France.
  • Lemonnier L; Association Vaincre la Mucoviscidose, Paris, France.
  • Burnet E; Respiratory Medicine and Cystic Fibrosis National Reference Center, Cochin Hospital, Assistance Publique Hôpitaux de Paris (AP-HP), Paris, France; ERN-Lung CF network, Frankfurt, Germany.
  • Paillasseur JL; Effi-stat, Paris, France.
  • Da Silva J; Respiratory Medicine and Cystic Fibrosis National Reference Center, Cochin Hospital, Assistance Publique Hôpitaux de Paris (AP-HP), Paris, France; ERN-Lung CF network, Frankfurt, Germany; URC-CIC Paris Descartes Necker Cochin, AP-HP, Hôpital Cochin, Paris, France.
  • Burgel PR; Université de Paris, Institut Cochin, Inserm U1016, Paris, France; Respiratory Medicine and Cystic Fibrosis National Reference Center, Cochin Hospital, Assistance Publique Hôpitaux de Paris (AP-HP), Paris, France; ERN-Lung CF network, Frankfurt, Germany. Electronic address: pierre-regis.burgel@aphp.
J Cyst Fibros ; 21(3): 489-496, 2022 05.
Article em En | MEDLINE | ID: mdl-35123901

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Transplante de Pulmão / Fibrose Cística Tipo de estudo: Diagnostic_studies / Prognostic_studies Limite: Humans Idioma: En Revista: J Cyst Fibros Ano de publicação: 2022 Tipo de documento: Article País de afiliação: Alemanha

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Transplante de Pulmão / Fibrose Cística Tipo de estudo: Diagnostic_studies / Prognostic_studies Limite: Humans Idioma: En Revista: J Cyst Fibros Ano de publicação: 2022 Tipo de documento: Article País de afiliação: Alemanha