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IPSC derived cardiac fibroblasts of DMD patients show compromised actin microfilaments, metabolic shift and pro-fibrotic phenotype.
Soussi, Salwa; Savchenko, Lesia; Rovina, Davide; Iacovoni, Jason S; Gottinger, Andrea; Vialettes, Maxime; Pioner, Josè-Manuel; Farini, Andrea; Mallia, Sara; Rabino, Martina; Pompilio, Giulio; Parini, Angelo; Lairez, Olivier; Gowran, Aoife; Pizzinat, Nathalie.
Afiliação
  • Soussi S; National Institute of Health and Medical Research (INSERM), I2MC, U1297, Toulouse, France.
  • Savchenko L; University Toulouse III, 118 route de Narbonne, 31062 Toulouse, CEDEX 9, Toulouse, France.
  • Rovina D; National Institute of Health and Medical Research (INSERM), I2MC, U1297, Toulouse, France.
  • Iacovoni JS; University Toulouse III, 118 route de Narbonne, 31062 Toulouse, CEDEX 9, Toulouse, France.
  • Gottinger A; Unit of Vascular Biology and Regenerative Medicine, Centro Cardiologico Monzino IRCCS, Milan, Italy.
  • Vialettes M; National Institute of Health and Medical Research (INSERM), I2MC, U1297, Toulouse, France.
  • Pioner JM; National Institute of Health and Medical Research (INSERM) U1297 I2MC, Bioinformatic Core Facility, I2MC, Toulouse, France.
  • Farini A; National Institute of Health and Medical Research (INSERM), I2MC, U1297, Toulouse, France.
  • Mallia S; University Toulouse III, 118 route de Narbonne, 31062 Toulouse, CEDEX 9, Toulouse, France.
  • Rabino M; Department of Biology, University of Florence, Florence, Italy.
  • Pompilio G; Neurology Unit, Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Milan, Italy.
  • Parini A; Unit of Vascular Biology and Regenerative Medicine, Centro Cardiologico Monzino IRCCS, Milan, Italy.
  • Lairez O; Unit of Vascular Biology and Regenerative Medicine, Centro Cardiologico Monzino IRCCS, Milan, Italy.
  • Gowran A; Unit of Vascular Biology and Regenerative Medicine, Centro Cardiologico Monzino IRCCS, Milan, Italy.
  • Pizzinat N; Department of Biomedical, Surgical and Dental Sciences, Università Degli Studi di Milano, Milan, Italy.
Biol Direct ; 18(1): 41, 2023 07 27.
Article em En | MEDLINE | ID: mdl-37501163

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Distrofia Muscular de Duchenne / Células-Tronco Pluripotentes Induzidas Limite: Humans Idioma: En Revista: Biol Direct Ano de publicação: 2023 Tipo de documento: Article País de afiliação: França

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Distrofia Muscular de Duchenne / Células-Tronco Pluripotentes Induzidas Limite: Humans Idioma: En Revista: Biol Direct Ano de publicação: 2023 Tipo de documento: Article País de afiliação: França