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Vasculitis and vasculopathy associated with inborn errors of immunity: an overview.
Federici, Silvia; Cinicola, Bianca Laura; La Torre, Francesco; Castagnoli, Riccardo; Lougaris, Vassilios; Giardino, Giuliana; Volpi, Stefano; Caorsi, Roberta; Leonardi, Lucia; Corrente, Stefania; Soresina, Annarosa; Cancrini, Caterina; Insalaco, Antonella; Gattorno, Marco; De Benedetti, Fabrizio; Marseglia, Gian Luigi; Del Giudice, Michele Miraglia; Cardinale, Fabio.
Afiliação
  • Federici S; Division of Rheumatology, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.
  • Cinicola BL; Department of Maternal Infantile and Urological Sciences, Sapienza University of Rome, Rome, Italy.
  • La Torre F; Department of Molecular Medicine, Sapienza University of Rome, Rome, Italy.
  • Castagnoli R; Department of Pediatrics, Giovanni XXIII Pediatric Hospital, University of Bari, Bari, Italy.
  • Lougaris V; Pediatric Unit, Department of Clinical, Surgical, Diagnostic, and Pediatric Sciences, University of Pavia, Pavia, Italy.
  • Giardino G; Pediatric Clinic, Fondazione IRCCS Policlinico San Matteo, Pavia, Italy.
  • Volpi S; Department of Clinical and Experimental Sciences, Pediatrics Clinic and Institute for Molecular Medicine A. Nocivelli, University of Brescia and ASST-Spedali Civili di Brescia, Brescia, Italy.
  • Caorsi R; Pediatric Section, Department of Translational Medical Sciences, Federico II University, Naples, Italy.
  • Leonardi L; Center for Autoinflammatory Diseases and Immunodeficiency, IRCCS Istituto Giannina Gaslini, Genoa, Italy.
  • Corrente S; Center for Autoinflammatory Diseases and Immunodeficiency, IRCCS Istituto Giannina Gaslini, Genoa, Italy.
  • Soresina A; Department of Maternal Infantile and Urological Sciences, Sapienza University of Rome, Rome, Italy.
  • Cancrini C; Division of Pediatrics, S. Camillo-Forlanini Hospital, Rome, Italy.
  • Insalaco A; Unit of Pediatric Immunology, Pediatrics Clinic, University of Brescia, ASST-Spedali Civili Brescia, Brescia, Italy.
  • Gattorno M; Department of Systems Medicine, University of Rome Tor Vergata, Rome, Italy.
  • De Benedetti F; Academic Department of Pediatrics, Immune and Infectious Diseases Division, Research Unit of Primary Immunodeficiencies, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.
  • Marseglia GL; Division of Rheumatology, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.
  • Del Giudice MM; Department of Maternal Infantile and Urological Sciences, Sapienza University of Rome, Rome, Italy.
  • Cardinale F; Division of Rheumatology, Bambino Gesù Children's Hospital, IRCCS, Rome, Italy.
Front Pediatr ; 11: 1258301, 2023.
Article em En | MEDLINE | ID: mdl-38357265
ABSTRACT
Systemic autoinflammatory diseases (SAIDs) are disorders of innate immunity, which are characterized by unprovoked recurrent flares of systemic inflammation often characterized by fever associated with clinical manifestations mainly involving the musculoskeletal, mucocutaneous, gastrointestinal, and nervous systems. Several conditions also present with varied, sometimes prominent, involvement of the vascular system, with features of vasculitis characterized by variable target vessel involvement and organ damage. Here, we report a systematic review of vasculitis and vasculopathy associated with inborn errors of immunity.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Tipo de estudo: Overview / Risk_factors_studies Idioma: En Revista: Front Pediatr Ano de publicação: 2023 Tipo de documento: Article País de afiliação: Itália

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Tipo de estudo: Overview / Risk_factors_studies Idioma: En Revista: Front Pediatr Ano de publicação: 2023 Tipo de documento: Article País de afiliação: Itália