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C9ORF72 patient-derived endothelial cells drive blood-brain barrier disruption and contribute to neurotoxicity.
Aragón-González, Ana; Shaw, Allan C; Kok, Jannigje R; Roussel, Florence S; Santos Souza, Cleide Dos; Granger, Sarah M; Vetter, Tatyana; de Diego, Yolanda; Meyer, Kathrin C; Beal, Selina N; Shaw, Pamela J; Ferraiuolo, Laura.
Afiliação
  • Aragón-González A; Sheffield Institute for Translational Neuroscience, University of Sheffield, 385 Glossop Road, S10 2HQ, Sheffield, UK. a.aragon@sheffield.ac.uk.
  • Shaw AC; Facultad de Medicina, Universidad de Málaga, 29010, Malaga, Spain. a.aragon@sheffield.ac.uk.
  • Kok JR; Center for Gene Therapy, The Abigail Wexner Research Institute, Nationwide Children's Hospital, OH 43205, Columbus, USA. a.aragon@sheffield.ac.uk.
  • Roussel FS; Sheffield Institute for Translational Neuroscience, University of Sheffield, 385 Glossop Road, S10 2HQ, Sheffield, UK.
  • Santos Souza CD; Sheffield Institute for Translational Neuroscience, University of Sheffield, 385 Glossop Road, S10 2HQ, Sheffield, UK.
  • Granger SM; Center for Gene Therapy, The Abigail Wexner Research Institute, Nationwide Children's Hospital, OH 43205, Columbus, USA.
  • Vetter T; Sheffield Institute for Translational Neuroscience, University of Sheffield, 385 Glossop Road, S10 2HQ, Sheffield, UK.
  • de Diego Y; Sheffield Institute for Translational Neuroscience, University of Sheffield, 385 Glossop Road, S10 2HQ, Sheffield, UK.
  • Meyer KC; Center for Gene Therapy, The Abigail Wexner Research Institute, Nationwide Children's Hospital, OH 43205, Columbus, USA.
  • Beal SN; Department of Pediatrics, The Ohio State University, Columbus, OH, USA.
  • Shaw PJ; Research Group PAIDI CTS-546, Institute of Biomedical Research of Málaga (IBIMA), 29010, Malaga, Spain.
  • Ferraiuolo L; Department of Cell Biology, Physiology, and Immunology, University of Córdoba, Campus Rabanales, Cordoba, Spain.
Fluids Barriers CNS ; 21(1): 34, 2024 Apr 11.
Article em En | MEDLINE | ID: mdl-38605366

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Barreira Hematoencefálica / Células Endoteliais / Esclerose Lateral Amiotrófica Limite: Humans Idioma: En Revista: Fluids Barriers CNS Ano de publicação: 2024 Tipo de documento: Article País de afiliação: Reino Unido

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Barreira Hematoencefálica / Células Endoteliais / Esclerose Lateral Amiotrófica Limite: Humans Idioma: En Revista: Fluids Barriers CNS Ano de publicação: 2024 Tipo de documento: Article País de afiliação: Reino Unido