RESUMEN
The superior vena cava syndrome (SVCS) is considered an emergency and requires immediate treatment; therefore, the etiologic diagnosis is essential before deciding on its implementation. The management of SVCS consists on the relief of symptoms and treatment of the underlying disease, aiming to restore the blood flow. We present a 5 years old boy with a history of B-cell ALL. His oncologic state was that of complete remission. In February 2013 he consulted for respiratory distress syndrome (RDS) of rapid evolution, and facial edema which progressed within 24 hours. CT chest and neck angiography was performed, showing pseudo nodular tissue compressing the SVC. Emergency endocavitary biopsy reported diffuse lymphoproliferative infiltration Chemotherapy is administered, with good results and hospital discharge. The SVCS is an oncologic emergency that requires prompt diagnosis and immediate treatment in order to improve results.
Asunto(s)
Neoplasias de la Médula Ósea/terapia , Neoplasias Cardíacas/diagnóstico , Recurrencia Local de Neoplasia/diagnóstico , Leucemia-Linfoma Linfoblástico de Células Precursoras/diagnóstico , Preescolar , Humanos , MasculinoRESUMEN
El síndrome de vena cava superior (SVCS), considerado una emergencia, requiere tratamiento inmediato, por lo que el diagnóstico etiológico es esencial antes de decidir una conducta terapéutica. El manejo del SVCS consiste en el alivio de los síntomas y de la enfermedad subyacente. Los tratamientos tienen el objetivo de restituir el flujo sanguíneo. Se presenta un paciente de 5 años de edad, masculino, con antecedente de LLA tipo B. Su estado oncohematológico era remisión total y, en febrero de 2013, consultó por síndrome de dificultad respiratoria (SDR) de rápida evolución y edema facial, que progresó en 24 h. Se realizó angio TC de tórax y vasos de cuello, que evidenció tejido pseudonodular que comprime VCS. Se realiza biopsia endocavitaria de urgencia, que informa infiltración difusa Knfroproliferativa. Tratamiento quimioterápico, con buena evolución y egreso hospitalario. El SVCS es una emergencia oncológica que requiere diagnóstico oportuno y tratamiento inmediato a fin de mejorar los resultados.
The superior vena cava syndrome (SVCS) is considered an emergency and requires immediate treatment; therefore, the etiologic diagnosis is essential before deciding on its implementation. The management of SVCS consists on the relief of symptoms and treatment of the underlying disease, aiming to restore the blood flow. We present a 5 years old boy with a history of B-cell ALL. His oncologic state was that of complete remission. In February 2013 he consulted for respiratory distress syndrome (RDS) of rapid evolution, and facial edema which progressed within 24 hours. CT chest and neck angiography was performed, showing pseudo nodular tissue compressing the SVC. Emergency endocavitary biopsy reported diffuse lymphoproliferative infiltration Chemotherapy is administered, with good results and hospital discharge. The SVCS is an oncologic emergency that requires prompt diagnosis and immediate treatment in order to improve results.
Asunto(s)
Preescolar , Humanos , Masculino , Neoplasias de la Médula Ósea/terapia , Neoplasias Cardíacas/diagnóstico , Recurrencia Local de Neoplasia/diagnóstico , Leucemia-Linfoma Linfoblástico de Células Precursoras/diagnósticoRESUMEN
El síndrome de vena cava superior (SVCS), considerado una emergencia, requiere tratamiento inmediato, por lo que el diagnóstico etiológico es esencial antes de decidir una conducta terapéutica. El manejo del SVCS consiste en el alivio de los síntomas y de la enfermedad subyacente. Los tratamientos tienen el objetivo de restituir el flujo sanguíneo. Se presenta un paciente de 5 años de edad, masculino, con antecedente de LLA tipo B. Su estado oncohematológico era remisión total y, en febrero de 2013, consultó por síndrome de dificultad respiratoria (SDR) de rápida evolución y edema facial, que progresó en 24 h. Se realizó angio TC de tórax y vasos de cuello, que evidenció tejido pseudonodular que comprime VCS. Se realiza biopsia endocavitaria de urgencia, que informa infiltración difusa Knfroproliferativa. Tratamiento quimioterápico, con buena evolución y egreso hospitalario. El SVCS es una emergencia oncológica que requiere diagnóstico oportuno y tratamiento inmediato a fin de mejorar los resultados.(AU)
The superior vena cava syndrome (SVCS) is considered an emergency and requires immediate treatment; therefore, the etiologic diagnosis is essential before deciding on its implementation. The management of SVCS consists on the relief of symptoms and treatment of the underlying disease, aiming to restore the blood flow. We present a 5 years old boy with a history of B-cell ALL. His oncologic state was that of complete remission. In February 2013 he consulted for respiratory distress syndrome (RDS) of rapid evolution, and facial edema which progressed within 24 hours. CT chest and neck angiography was performed, showing pseudo nodular tissue compressing the SVC. Emergency endocavitary biopsy reported diffuse lymphoproliferative infiltration Chemotherapy is administered, with good results and hospital discharge. The SVCS is an oncologic emergency that requires prompt diagnosis and immediate treatment in order to improve results.(AU)
RESUMEN
The superior vena cava syndrome (SVCS) is considered an emergency and requires immediate treatment; therefore, the etiologic diagnosis is essential before deciding on its implementation. The management of SVCS consists on the relief of symptoms and treatment of the underlying disease, aiming to restore the blood flow. We present a 5 years old boy with a history of B-cell ALL. His oncologic state was that of complete remission. In February 2013 he consulted for respiratory distress syndrome (RDS) of rapid evolution, and facial edema which progressed within 24 hours. CT chest and neck angiography was performed, showing pseudo nodular tissue compressing the SVC. Emergency endocavitary biopsy reported diffuse lymphoproliferative infiltration Chemotherapy is administered, with good results and hospital discharge. The SVCS is an oncologic emergency that requires prompt diagnosis and immediate treatment in order to improve results.