1.
Clin Pediatr (Phila)
; 22(1): 75-8, 1983 Jan.
Artigo
em Inglês
| MEDLINE
| ID: mdl-6848293
RESUMO
A case is reported of an infant with features of Noonan Syndrome and congenital pulmonary lymphangiectasis. Soon after birth, persistent respiratory distress developed, and, at 4 months of ge, a chylothorax was noted. Medium chain triglyceride therapy by the enteral route was tried, but parenteral alimentation and chest-tube drainage were required. Diagnosis of pulmonary lymphangiectasis was confirmed by biopsy.