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Megalencephalic leukoencephalopathy with subcortical cysts protein-1 modulates endosomal pH and protein trafficking in astrocytes: relevance to MLC disease pathogenesis.
Brignone, Maria S; Lanciotti, Angela; Visentin, Sergio; De Nuccio, Chiara; Molinari, Paola; Camerini, Serena; Diociaiuti, Marco; Petrini, Stefania; Minnone, Gaetana; Crescenzi, Marco; Laudiero, Luisa Bracci; Bertini, Enrico; Petrucci, Tamara C; Ambrosini, Elena.
Afiliación
  • Brignone MS; Department of Cell Biology and Neuroscience, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy. Electronic address: mariastefania.brignone@gmail.com.
  • Lanciotti A; Department of Cell Biology and Neuroscience, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy. Electronic address: angela.lanciotti@iss.it.
  • Visentin S; Department of Cell Biology and Neuroscience, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy. Electronic address: sergio.visentin@iss.it.
  • De Nuccio C; Department of Cell Biology and Neuroscience, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy. Electronic address: chiara.denuccio@iss.it.
  • Molinari P; Department of Pharmacology, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy. Electronic address: paola.molinari@iss.it.
  • Camerini S; Department of Cell Biology and Neuroscience, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy. Electronic address: serena.camerini@iss.it.
  • Diociaiuti M; Department of Technology and Health, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy. Electronic address: marco.diociaiuti@iss.it.
  • Petrini S; Unit of Neurodegenerative Disorders, Laboratory of Molecular Medicine, Bambino Gesù Pediatric Research Hospital, Piazza S. Onofrio 4, 00165 Rome, Italy. Electronic address: stefania.petrini@opbg.net.
  • Minnone G; Unit of Neurodegenerative Disorders, Laboratory of Molecular Medicine, Bambino Gesù Pediatric Research Hospital, Piazza S. Onofrio 4, 00165 Rome, Italy. Electronic address: gaetana.minnone@yahoo.it.
  • Crescenzi M; Department of Cell Biology and Neuroscience, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy. Electronic address: marco.crescenzi@iss.it.
  • Laudiero LB; Unit of Neurodegenerative Disorders, Laboratory of Molecular Medicine, Bambino Gesù Pediatric Research Hospital, Piazza S. Onofrio 4, 00165 Rome, Italy; Institute of Translational Pharmacology, CNR, Via del Fosso Cavaliere 100, 00133 Rome, Italy. Electronic address: luisa.braccilaudiero@inmm.cnr.it.
  • Bertini E; Unit of Neurodegenerative Disorders, Laboratory of Molecular Medicine, Bambino Gesù Pediatric Research Hospital, Piazza S. Onofrio 4, 00165 Rome, Italy. Electronic address: ebertini@gmail.com.
  • Petrucci TC; Department of Cell Biology and Neuroscience, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy. Electronic address: tcpetrucci.petrucci61@gmail.com.
  • Ambrosini E; Department of Cell Biology and Neuroscience, Istituto Superiore di Sanità, Viale Regina Elena 299, 00161 Rome, Italy. Electronic address: elena.ambrosini@iss.it.
Neurobiol Dis ; 66: 1-18, 2014 Jun.
Article en En | MEDLINE | ID: mdl-24561067

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Endosomas / Astrocitos / Transporte de Proteínas / Proteínas de la Membrana Tipo de estudio: Etiology_studies / Prognostic_studies Límite: Animals / Humans Idioma: En Revista: Neurobiol Dis Asunto de la revista: NEUROLOGIA Año: 2014 Tipo del documento: Article

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Endosomas / Astrocitos / Transporte de Proteínas / Proteínas de la Membrana Tipo de estudio: Etiology_studies / Prognostic_studies Límite: Animals / Humans Idioma: En Revista: Neurobiol Dis Asunto de la revista: NEUROLOGIA Año: 2014 Tipo del documento: Article