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Deficiency Mutations of Alpha-1 Antitrypsin. Effects on Folding, Function, and Polymerization.
Haq, Imran; Irving, James A; Saleh, Aarash D; Dron, Louis; Regan-Mochrie, Gemma L; Motamedi-Shad, Neda; Hurst, John R; Gooptu, Bibek; Lomas, David A.
Afiliación
  • Haq I; 1 Wolfson Institute for Biomedical Research, University College London, London, United Kingdom.
  • Irving JA; 2 Institute of Structural and Molecular Biology/Birkbeck, University of London, London, United Kingdom.
  • Saleh AD; 1 Wolfson Institute for Biomedical Research, University College London, London, United Kingdom.
  • Dron L; 2 Institute of Structural and Molecular Biology/Birkbeck, University of London, London, United Kingdom.
  • Regan-Mochrie GL; 3 London Alpha-1 Antitrypsin Deficiency Service, Royal Free Hospital, Pond Street, London, United Kingdom; and.
  • Motamedi-Shad N; 3 London Alpha-1 Antitrypsin Deficiency Service, Royal Free Hospital, Pond Street, London, United Kingdom; and.
  • Hurst JR; 1 Wolfson Institute for Biomedical Research, University College London, London, United Kingdom.
  • Gooptu B; 1 Wolfson Institute for Biomedical Research, University College London, London, United Kingdom.
  • Lomas DA; 2 Institute of Structural and Molecular Biology/Birkbeck, University of London, London, United Kingdom.
Am J Respir Cell Mol Biol ; 54(1): 71-80, 2016 Jan.
Article en En | MEDLINE | ID: mdl-26091018

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Alfa 1-Antitripsina / Deficiencia de alfa 1-Antitripsina / Mutación Tipo de estudio: Prognostic_studies Límite: Adult / Female / Humans Idioma: En Revista: Am J Respir Cell Mol Biol Asunto de la revista: BIOLOGIA MOLECULAR Año: 2016 Tipo del documento: Article País de afiliación: Reino Unido

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Alfa 1-Antitripsina / Deficiencia de alfa 1-Antitripsina / Mutación Tipo de estudio: Prognostic_studies Límite: Adult / Female / Humans Idioma: En Revista: Am J Respir Cell Mol Biol Asunto de la revista: BIOLOGIA MOLECULAR Año: 2016 Tipo del documento: Article País de afiliación: Reino Unido