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ALS mouse model SOD1G93A displays early pathology of sensory small fibers associated to accumulation of a neurotoxic splice variant of peripherin.
Sassone, Jenny; Taiana, Michela; Lombardi, Raffaella; Porretta-Serapiglia, Carla; Freschi, Mattia; Bonanno, Silvia; Marcuzzo, Stefania; Caravello, Francesca; Bendotti, Caterina; Lauria, Giuseppe.
Afiliación
  • Sassone J; 3rd Neurology Unit and jenny.sassone@istituto-besta.it glauria@istituto-besta.it.
  • Taiana M; 3rd Neurology Unit and.
  • Lombardi R; 3rd Neurology Unit and.
  • Porretta-Serapiglia C; 3rd Neurology Unit and.
  • Freschi M; Neuroscience Department, Laboratory of Molecular Neurobiology, IRCCS Istituto di Ricerche Farmacologiche 'Mario Negri', Animal Facility Fondazione italiana per la ricerca sulla SLA (AriSLA), Milan, Italy and.
  • Bonanno S; 4th Neurology Unit, IRCCS Foundation 'Carlo Besta' Neurological Institute, via Celoria 11, 20133 Milan, Italy, PhD Program in Neuroscience, University of Milan, Bicocca, Italy.
  • Marcuzzo S; 4th Neurology Unit, IRCCS Foundation 'Carlo Besta' Neurological Institute, via Celoria 11, 20133 Milan, Italy.
  • Caravello F; 3rd Neurology Unit and.
  • Bendotti C; Neuroscience Department, Laboratory of Molecular Neurobiology, IRCCS Istituto di Ricerche Farmacologiche 'Mario Negri'.
  • Lauria G; 3rd Neurology Unit and jenny.sassone@istituto-besta.it glauria@istituto-besta.it.
Hum Mol Genet ; 25(8): 1588-99, 2016 Apr 15.
Article en En | MEDLINE | ID: mdl-26908600

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Empalme Alternativo / Sustitución de Aminoácidos / Periferinas / Superóxido Dismutasa-1 / Ganglios Espinales / Esclerosis Amiotrófica Lateral Tipo de estudio: Prognostic_studies / Risk_factors_studies Límite: Animals / Humans Idioma: En Revista: Hum Mol Genet Asunto de la revista: BIOLOGIA MOLECULAR / GENETICA MEDICA Año: 2016 Tipo del documento: Article

Texto completo: 1 Colección: 01-internacional Banco de datos: MEDLINE Asunto principal: Empalme Alternativo / Sustitución de Aminoácidos / Periferinas / Superóxido Dismutasa-1 / Ganglios Espinales / Esclerosis Amiotrófica Lateral Tipo de estudio: Prognostic_studies / Risk_factors_studies Límite: Animals / Humans Idioma: En Revista: Hum Mol Genet Asunto de la revista: BIOLOGIA MOLECULAR / GENETICA MEDICA Año: 2016 Tipo del documento: Article