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Powerhouse failure and oxidative damage in autosomal recessive spastic ataxia of Charlevoix-Saguenay.
Criscuolo, Chiara; Procaccini, C; Meschini, M C; Cianflone, A; Carbone, R; Doccini, S; Devos, D; Nesti, C; Vuillaume, I; Pellegrino, M; Filla, A; De Michele, G; Matarese, G; Santorelli, F M.
Afiliação
  • Criscuolo C; Department of Neurosciences, Reproductive and Odontostomatological Sciences, Federico II University, Via Pansini 5, 80131, Naples, Italy. sky569@libero.it.
  • Procaccini C; Laboratory of Immunology, Institute of Experimental Endocrinology and Oncology, National Research Council (IEOS-CNR) c/o Department of Molecular Medicine and Medical Biotechnology, Federico II University, Naples, Italy.
  • Meschini MC; Molecular Medicine and Neuromuscular Laboratory, IRCCS Stella Maris, Pisa, Italy.
  • Cianflone A; Department of Neurosciences, Reproductive and Odontostomatological Sciences, Federico II University, Via Pansini 5, 80131, Naples, Italy.
  • Carbone R; Department of Neurosciences, Reproductive and Odontostomatological Sciences, Federico II University, Via Pansini 5, 80131, Naples, Italy.
  • Doccini S; Molecular Medicine and Neuromuscular Laboratory, IRCCS Stella Maris, Pisa, Italy.
  • Devos D; Medical Pharmacology, Department of Neurology, CHRU University of Lille 2, Lille, France.
  • Nesti C; Molecular Medicine and Neuromuscular Laboratory, IRCCS Stella Maris, Pisa, Italy.
  • Vuillaume I; Department of Neurobiology, Center of Biology-Pathology, CHRU University of Lille 2, Lille, France.
  • Pellegrino M; Translational Research and New Technologies in Medicine and Surgery, University of Pisa, Pisa, Italy.
  • Filla A; Department of Neurosciences, Reproductive and Odontostomatological Sciences, Federico II University, Via Pansini 5, 80131, Naples, Italy.
  • De Michele G; Department of Neurosciences, Reproductive and Odontostomatological Sciences, Federico II University, Via Pansini 5, 80131, Naples, Italy.
  • Matarese G; Department of Medicine and Surgery, University of Salerno, Salerno, Italy.
  • Santorelli FM; IRCCS Multimedica, Milan, Italy.
J Neurol ; 262(12): 2755-63, 2015 Dec.
Article em En | MEDLINE | ID: mdl-26530509

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Pele / Estresse Oxidativo / Ataxias Espinocerebelares / Doenças Mitocondriais / Fibroblastos / Espasticidade Muscular Tipo de estudo: Etiology_studies Limite: Adult / Female / Humans / Male / Middle aged Idioma: En Revista: J Neurol Ano de publicação: 2015 Tipo de documento: Article País de afiliação: Itália

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Pele / Estresse Oxidativo / Ataxias Espinocerebelares / Doenças Mitocondriais / Fibroblastos / Espasticidade Muscular Tipo de estudo: Etiology_studies Limite: Adult / Female / Humans / Male / Middle aged Idioma: En Revista: J Neurol Ano de publicação: 2015 Tipo de documento: Article País de afiliação: Itália