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Suppressing UPR-dependent overactivation of FGFR3 signaling ameliorates SLC26A2-deficient chondrodysplasias.
Zheng, Chao; Lin, Xisheng; Xu, Xiaolong; Wang, Cheng; Zhou, Jinru; Gao, Bo; Fan, Jing; Lu, Weiguang; Hu, Yaqian; Jie, Qiang; Luo, Zhuojing; Yang, Liu.
Afiliação
  • Zheng C; Institute of Orthopedic Surgery, Xijing Hospital, Fourth Military Medical University, Xi'an, China.
  • Lin X; Institute of Orthopedic Surgery, Xijing Hospital, Fourth Military Medical University, Xi'an, China.
  • Xu X; Institute of Orthopedic Surgery, Xijing Hospital, Fourth Military Medical University, Xi'an, China.
  • Wang C; School of Biomedical Sciences, University of Hong Kong, Hong Kong, China.
  • Zhou J; Institute of Orthopedic Surgery, Xijing Hospital, Fourth Military Medical University, Xi'an, China.
  • Gao B; Institute of Orthopedic Surgery, Xijing Hospital, Fourth Military Medical University, Xi'an, China.
  • Fan J; Institute of Orthopedic Surgery, Xijing Hospital, Fourth Military Medical University, Xi'an, China.
  • Lu W; Institute of Orthopedic Surgery, Xijing Hospital, Fourth Military Medical University, Xi'an, China.
  • Hu Y; Institute of Orthopedic Surgery, Xijing Hospital, Fourth Military Medical University, Xi'an, China.
  • Jie Q; Department of Orthopedic Surgery, HongHui Hospital, Xi'an Jiaotong University, College of Medicine, Xi'an, China.
  • Luo Z; Institute of Orthopedic Surgery, Xijing Hospital, Fourth Military Medical University, Xi'an, China; Medical Research Institute, Northwestern Polytechnical University, Xi'an, China.
  • Yang L; Institute of Orthopedic Surgery, Xijing Hospital, Fourth Military Medical University, Xi'an, China; Medical Research Institute, Northwestern Polytechnical University, Xi'an, China. Electronic address: yangliu@fmmu.edu.cn.
EBioMedicine ; 40: 695-709, 2019 Feb.
Article em En | MEDLINE | ID: mdl-30685387

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Acondroplasia / Transdução de Sinais / Receptor Tipo 3 de Fator de Crescimento de Fibroblastos / Resposta a Proteínas não Dobradas / Transportadores de Sulfato Tipo de estudo: Prognostic_studies Limite: Animals / Humans Idioma: En Revista: EBioMedicine Ano de publicação: 2019 Tipo de documento: Article País de afiliação: China

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Acondroplasia / Transdução de Sinais / Receptor Tipo 3 de Fator de Crescimento de Fibroblastos / Resposta a Proteínas não Dobradas / Transportadores de Sulfato Tipo de estudo: Prognostic_studies Limite: Animals / Humans Idioma: En Revista: EBioMedicine Ano de publicação: 2019 Tipo de documento: Article País de afiliação: China