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Nuclear Factor-κB Pathway Mediates the Molecular Pathogenesis of LMNA-Related Muscular Dystrophies.
Fan, Yanbin; Tan, Dandan; Zhang, Xu; Song, Danyu; Chang, Xingzhi; Wang, Shuang; Yan, Hui; Ge, Lin; Yang, Haipo; Bönnemann, Carsten; Liu, Jingying; Wang, Suxia; Wu, Xiru; Zhang, Hong; Xiong, Hui.
Afiliação
  • Fan Y; Department of Pediatrics, Peking University First Hospital, No.1 Xi'an Men Street, West District, Beijing, 100034, People's Republic of China.
  • Tan D; Department of Pediatrics, Peking University First Hospital, No.1 Xi'an Men Street, West District, Beijing, 100034, People's Republic of China.
  • Zhang X; Department of Neurology, Jiujiang University Clinical Medical College, Jiujiang University Hospital, Jiujiang, Jiangxi, 332000, People's Republic of China.
  • Song D; Center of Ultrastructural Pathology, Lab of Electron Microscopy, Peking University First Hospital, Beijing, 100034, People's Republic of China.
  • Chang X; Department of Pediatrics, Peking University First Hospital, No.1 Xi'an Men Street, West District, Beijing, 100034, People's Republic of China.
  • Wang S; Department of Pediatrics, Peking University First Hospital, No.1 Xi'an Men Street, West District, Beijing, 100034, People's Republic of China.
  • Yan H; Department of Pediatrics, Peking University First Hospital, No.1 Xi'an Men Street, West District, Beijing, 100034, People's Republic of China.
  • Ge L; Department of Pediatrics, Peking University First Hospital, No.1 Xi'an Men Street, West District, Beijing, 100034, People's Republic of China.
  • Yang H; Department of Pediatrics, Peking University First Hospital, No.1 Xi'an Men Street, West District, Beijing, 100034, People's Republic of China.
  • Bönnemann C; Department of Pediatrics, Peking University First Hospital, No.1 Xi'an Men Street, West District, Beijing, 100034, People's Republic of China.
  • Liu J; Neuromuscular and Neurogenetic Disorders of Childhood Section, National Institute of Neurological Disorders and Stroke, National Institutes of Health, Bethesda, MD, USA.
  • Wang S; Institute of Cardiovascular Sciences and Key Laboratory of Molecular Cardiovascular Sciences, Peking University Health Science Center, No.38 Xueyuan Road, Haidian District, Beijing, 100191, People's Republic of China.
  • Wu X; Center of Ultrastructural Pathology, Lab of Electron Microscopy, Peking University First Hospital, Beijing, 100034, People's Republic of China.
  • Zhang H; Department of Pediatrics, Peking University First Hospital, No.1 Xi'an Men Street, West District, Beijing, 100034, People's Republic of China.
  • Xiong H; Institute of Cardiovascular Sciences and Key Laboratory of Molecular Cardiovascular Sciences, Peking University Health Science Center, No.38 Xueyuan Road, Haidian District, Beijing, 100191, People's Republic of China. zhanghong@bjmu.edu.cn.
Biochem Genet ; 58(6): 966-980, 2020 Dec.
Article em En | MEDLINE | ID: mdl-32705401

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Transdução de Sinais / NF-kappa B / Mutação de Sentido Incorreto / Lamina Tipo A / Laminopatias / Distrofias Musculares Tipo de estudo: Etiology_studies Limite: Humans Idioma: En Revista: Biochem Genet Ano de publicação: 2020 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Transdução de Sinais / NF-kappa B / Mutação de Sentido Incorreto / Lamina Tipo A / Laminopatias / Distrofias Musculares Tipo de estudo: Etiology_studies Limite: Humans Idioma: En Revista: Biochem Genet Ano de publicação: 2020 Tipo de documento: Article