Simultaneous LeFort III and LeFort I Osteotomies in Craniometaphyseal Dysplasia.
Cleft Palate Craniofac J
; 58(12): 1560-1568, 2021 12.
Article
em En
| MEDLINE
| ID: mdl-33563004
ABSTRACT
Craniometaphyseal dysplasia (CMD) is a rare genetic disease affecting bone metabolism with sclerosis of craniofacial bones. Orthognathic surgery has rarely been described in this patient population due to the bony thickness, making osteotomies challenging. We present a 19-year-old male with CMD with malocclusion, severe midface hypoplasia, and obstructive sleep apnea. With the aid virtual planning, we safely performed a combined LeFort III/I midface advancement to correct a negative overjet to improve occlusal balance, decrease scleral show, and diminish daytime sleepiness.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Anormalidades Craniofaciais
/
Procedimentos Cirúrgicos Ortognáticos
/
Hipertelorismo
Limite:
Adult
/
Humans
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Male
Idioma:
En
Revista:
Cleft Palate Craniofac J
Assunto da revista:
ODONTOLOGIA
Ano de publicação:
2021
Tipo de documento:
Article
País de afiliação:
Estados Unidos