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Increased Reactive Oxygen Species-Mediated Ca2+/Calmodulin-Dependent Protein Kinase II Activation Contributes to Calcium Handling Abnormalities and Impaired Contraction in Barth Syndrome.
Liu, Xujie; Wang, Suya; Guo, Xiaoling; Li, Yifei; Ogurlu, Roza; Lu, Fujian; Prondzynski, Maksymilian; de la Serna Buzon, Sofia; Ma, Qing; Zhang, Donghui; Wang, Gang; Cotton, Justin; Guo, Yuxuan; Xiao, Ling; Milan, David J; Xu, Yang; Schlame, Michael; Bezzerides, Vassilios J; Pu, William T.
Afiliação
  • Liu X; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • Wang S; Department of Radiology, Basic Medical School, Chongqing Medical University, China (X.L.).
  • Guo X; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • Li Y; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • Ogurlu R; Center of Scientific Research, the Second Affiliated Hospital and Yuying Children's Hospital of Wenzhou Medical University, Zhejiang, China (X.G.).
  • Lu F; Key Laboratory of Birth Defects and Related Diseases of Women and Children of MOE, Department of Pediatrics, West China Second University Hospital, Sichuan University, Chengdu (Y.L.).
  • Prondzynski M; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • de la Serna Buzon S; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • Ma Q; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • Zhang D; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • Wang G; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • Cotton J; State Key Laboratory of Biocatalysis and Enzyme Engineering, School of Life Science, Hubei University, Wuhan, China (D.Z.).
  • Guo Y; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • Xiao L; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • Milan DJ; Harvard College, Cambridge, MA (J.C.).
  • Xu Y; Department of Cardiology, Boston Children's Hospital, MA (X.L., S.W., X.G., R.O., F.L., M.P., S.d.l.S.B., Q.M., G.W., J.C., Y.G., V.J.B., W.T.P.).
  • Schlame M; Department of Cardiology, Massachusetts General Hospital, Boston (L.X., D.J.M.).
  • Bezzerides VJ; Department of Cardiology, Massachusetts General Hospital, Boston (L.X., D.J.M.).
  • Pu WT; Department of Anesthesiology, New York University School of Medicine (Y.X., M.S.).
Circulation ; 143(19): 1894-1911, 2021 05 11.
Article em En | MEDLINE | ID: mdl-33793303

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Cálcio / Espécies Reativas de Oxigênio / Proteína Quinase Tipo 2 Dependente de Cálcio-Calmodulina / Síndrome de Barth Tipo de estudo: Prognostic_studies Limite: Animals / Humans Idioma: En Revista: Circulation Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Cálcio / Espécies Reativas de Oxigênio / Proteína Quinase Tipo 2 Dependente de Cálcio-Calmodulina / Síndrome de Barth Tipo de estudo: Prognostic_studies Limite: Animals / Humans Idioma: En Revista: Circulation Ano de publicação: 2021 Tipo de documento: Article