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Disease Progression of WHIM Syndrome in an International Cohort of 66 Pediatric and Adult Patients.
Geier, Christoph B; Ellison, Maryssa; Cruz, Rachel; Pawar, Sumit; Leiss-Piller, Alexander; Zmajkovicova, Katarina; McNulty, Shannon M; Yilmaz, Melis; Evans, Martin Oman; Gordon, Sumai; Ujhazi, Boglarka; Wiest, Ivana; Abolhassani, Hassan; Aghamohammadi, Asghar; Barmettler, Sara; Bhar, Saleh; Bondarenko, Anastasia; Bolyard, Audrey Anna; Buchbinder, David; Cada, Michaela; Cavieres, Mirta; Connelly, James A; Dale, David C; Deordieva, Ekaterina; Dorsey, Morna J; Drysdale, Simon B; Ehl, Stephan; Elfeky, Reem; Fioredda, Francesca; Firkin, Frank; Förster-Waldl, Elizabeth; Geng, Bob; Goda, Vera; Gonzalez-Granado, Luis; Grunebaum, Eyal; Grzesk, Elzbieta; Henrickson, Sarah E; Hilfanova, Anna; Hiwatari, Mitsuteru; Imai, Chihaya; Ip, Winnie; Jyonouchi, Soma; Kanegane, Hirokazu; Kawahara, Yuta; Khojah, Amer M; Kim, Vy Hong-Diep; Kojic, Marina; Koltan, Sylwia; Krivan, Gergely; Langguth, Daman.
Afiliação
  • Geier CB; Institute for Immunodeficiency, Center for Chronic Immunodeficiency, Medical Center University of Freiburg Faculty of Medicine, University of Freiburg, Freiburg, Germany.
  • Ellison M; Department of Rheumatology and Clinical Immunology, Center for Chronic Immunodeficiency, Medical Center University of Freiburg, Faculty of Medicine, University of Freiburg, Freiburg, Germany.
  • Cruz R; Division of Pediatric Allergy and Immunology, Department of Pediatrics, University of South Florida, St. Petersburg, FL, USA.
  • Pawar S; Division of Pediatric Allergy and Immunology, Department of Pediatrics, University of South Florida, St. Petersburg, FL, USA.
  • Leiss-Piller A; Morsani College of Medicine, University of South Florida, Tampa, FL, USA.
  • Zmajkovicova K; X4 Pharmaceuticals (Austria) GmbH, Vienna, Austria.
  • McNulty SM; Immunology Outpatient Clinic, Vienna, Austria.
  • Yilmaz M; X4 Pharmaceuticals (Austria) GmbH, Vienna, Austria.
  • Evans MO; Department of Genetics, University of North Carolina at Chapel Hill, Chapel Hill, NC, USA.
  • Gordon S; Division of Pediatric Allergy and Immunology, Department of Pediatrics, University of South Florida, St. Petersburg, FL, USA.
  • Ujhazi B; Blanchfield Army Community Hospital, Fort Campbell, KY, USA.
  • Wiest I; Division of Pediatric Allergy and Immunology, Department of Pediatrics, University of South Florida, St. Petersburg, FL, USA.
  • Abolhassani H; Division of Pediatric Allergy and Immunology, Department of Pediatrics, University of South Florida, St. Petersburg, FL, USA.
  • Aghamohammadi A; X4 Pharmaceuticals (Austria) GmbH, Vienna, Austria.
  • Barmettler S; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Bhar S; Division of Clinical Immunology, Department of Laboratory Medicine, Karolinska Institute at Karolinska University Hospital Huddinge, Stockholm, Sweden.
  • Bondarenko A; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Bolyard AA; Allergy and Clinical Immunology Unit, Division of Rheumatology, Allergy & Immunology, Massachusetts General Hospital, Boston, MA, USA.
  • Buchbinder D; Department of Pediatrics, Section of Hematology/Oncology and Critical Care Medicine, Bone Marrow Transplantation, Baylor College of Medicine, Texas Children's Hospital, Houston, TX, USA.
  • Cada M; Shupyk National Medical Academy of Postgraduate Education, Kyiv, Ukraine.
  • Cavieres M; Severe Chronic Neutropenia International Registry, University of Washington, Seattle, WA, USA.
  • Connelly JA; Division of Hematology, CHOC Children's Hospital, Orange, CA, USA.
  • Dale DC; Division of Hematology and Oncology, Hospital for Sick Children, Toronto, Ontario, Canada.
  • Deordieva E; Department of Pediatrics, University of Toronto, Toronto, Ontario, Canada.
  • Dorsey MJ; Hematology Unit, Dr Luis Calvo Mackenna Children's Hospital, Santiago, Chile.
  • Drysdale SB; Vanderbilt University Medical Center, Nashville, TN, USA.
  • Ehl S; Department of Medicine, University of Washington, Seattle, WA, USA.
  • Elfeky R; Immunology, the Dmitry Rogachev National Medical Center of Pediatric Hematology, Oncology and Immunology, Moscow, Russia.
  • Fioredda F; Division of Allergy, Immunology and Blood and Marrow Transplantation, Department of Pediatrics, UCSF Benioff Children's Hospital, San Francisco, CA, USA.
  • Firkin F; Paediatric Infectious Diseases Research Group, St George's University Hospitals NHS Foundation Trust, London, UK.
  • Förster-Waldl E; Institute for Immunodeficiency, Center for Chronic Immunodeficiency, Medical Center University of Freiburg Faculty of Medicine, University of Freiburg, Freiburg, Germany.
  • Geng B; Department of Clinical Immunology, Royal Free Hospital, London, UK.
  • Goda V; Haematology Unit, IRCCS Istituto Giannina Gaslini, Genoa, Italy.
  • Gonzalez-Granado L; Department of Medicine, St Vincent's Hospital, University of Melbourne, Vic, Fitzroy, Australia.
  • Grunebaum E; Department of Clinical Haematology, St Vincent's Hospital, Vic, Fitzroy, Australia.
  • Grzesk E; Department of Pediatrics and Adolescent Medicine, Medical University of Vienna, Vienna, Austria.
  • Henrickson SE; Division of Neonatology, Pediatric Intensive Care & Neuropediatrics, Department of Pediatrics and Adolescent Medicine, Medical University of Vienna, Vienna, Austria.
  • Hilfanova A; Center for Congenital Immunodeficiencies, Medical University of Vienna & Jeffrey Modell Diagnostic and Research Center, Vienna, Austria.
  • Hiwatari M; Divisions of Adult and Pediatric Allergy and Immunology, University of California, San Diego, CA, USA.
  • Imai C; Department for Pediatric Hematology and Hemopoietic Stem Cell Transplantation, Central Hospital of Southern Pest - National Institute of Hematology and Infectious Diseases, Budapest, Hungary.
  • Ip W; Immunodeficiencies Unit, Department of Pediatrics, University Hospital 12 de Octubre, Research Institute Hospital 12 Octubre, Madrid, Spain.
  • Jyonouchi S; Department of Pediatrics, University of Toronto, Toronto, Ontario, Canada.
  • Kanegane H; Division of Immunology and Allergy, Hospital for Sick Children, Toronto, Ontario, Canada.
  • Kawahara Y; Department of Pediatrics, Hematology and Oncology Collegium Medicum, Bydgoszcz Nicolaus Copernicus University, Torun, Poland.
  • Khojah AM; Division of Allergy and Immunology, Children's Hospital of Philadelphia, Philadelphia, PA, USA.
  • Kim VH; Department of Pediatrics, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.
  • Kojic M; Institute for Immunology, Perelman School of Medicine, University of Pennsylvania, Philadelphia, PA, USA.
  • Koltan S; Shupyk National Medical Academy of Postgraduate Education, Kyiv, Ukraine.
  • Krivan G; Department of Pediatrics, Graduate School of Medicine, The University of Tokyo, Tokyo, Japan.
  • Langguth D; Department of Pediatrics, Niigata University Graduate School of Medical and Dental Sciences, Niigata, Japan.
J Clin Immunol ; 42(8): 1748-1765, 2022 11.
Article em En | MEDLINE | ID: mdl-35947323

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Verrugas / Agamaglobulinemia / Síndromes de Imunodeficiência / Linfopenia / Neutropenia Tipo de estudo: Diagnostic_studies / Risk_factors_studies Limite: Humans Idioma: En Revista: J Clin Immunol Ano de publicação: 2022 Tipo de documento: Article País de afiliação: Alemanha

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Verrugas / Agamaglobulinemia / Síndromes de Imunodeficiência / Linfopenia / Neutropenia Tipo de estudo: Diagnostic_studies / Risk_factors_studies Limite: Humans Idioma: En Revista: J Clin Immunol Ano de publicação: 2022 Tipo de documento: Article País de afiliação: Alemanha