Double-outlet left ventricle. Echocardiographic diagnosis.

This is a case report of a double-outlet left ventricle associated with tricuspid atresia and hypoplasia of the right ventricle, diagnosed during echocardiography with color-flow imaging, in a three-month-old child who presented with fatigue and cyanosis. The child underwent palliative pulmonary arterial banding without an invasive procedure, and showed sustained improvement during follow-up.

[Surgical treatment of total anomalous drainage of pulmonary veins into the right superior vena cava]. / Tratamento cirúrgico de drenagem anômala total de veias pulmonares em veia cava superior direita.

This report describes a 2-month-old boy with diagnosis of total anomalous pulmonary venous obstruction and marked hypertension established by cross-sectioned echocardiography and catheterization with angiography. Successful surgical correction was performed with profound hypothermia and circulatory arrest. The risk factors and the high operative mortality associated with this type of anomaly are analyzed.

[Supravalvar and valvar aortic stenosis associated with valvar and subvalvar pulmonary stenosis. Coexistence of two clinical syndromes]. / Estenose supravalvar e valvar aórtica associada à estenose infundíbulo valvar pulmonar. Coexistência de duas síndromes clínicas.

A 4 year old patient with congenital rubella syndrome, confirmed serologically, presents with neurosensorial deafness and a rare association of cardiac anomalies: supravalvar and valvar aortic stenosis and subvalvar pulmonary stenosis. Bidimensional echocardiography and angiography confirmed the diagnosis and the surgical treatment was successful. Due to the presence of somatic characteristics of Williams's syndrome, mental retardation and supraortic stenosis, the authors postulate that there is a coexistence of clinical syndromes responsible for the malformations of this case. This fact is rare on clinical settings, requiring accurate diagnosis and treatment.