A case of CREST syndrome and myeloperoxidase-specific anti-neutrophil cytoplasmic autoantibody-associated glomerulonephritis.
Clin Nephrol
; 53(4): 296-300, 2000 Apr.
Article
em En
| MEDLINE
| ID: mdl-10809419
ABSTRACT
We report the first case of myeloperoxidase-specific anti-neutrophil cytoplasmic autoantibody (MPO-ANCA)-associated glomerulonephritis in a patient with CREST syndrome. A 74-year-old Japanese man with CREST syndrome (calcinosis, Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, and telangiectasia) developed rapidly progressive renal failure without elevation of blood pressure. Renal biopsy revealed glomerular sclerosis and fibrous crescents. The MPO-ANCA titer was elevated to 145 EU/ml. When patients with collagen diseases develop rapidly progressive glomerulonephritis, the possibility of MPO-ANCA-associated glomerulonephritis should be kept in mind.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Síndrome CREST
/
Peroxidase
/
Anticorpos Anticitoplasma de Neutrófilos
/
Glomerulonefrite
Tipo de estudo:
Risk_factors_studies
Limite:
Aged
/
Humans
/
Male
Idioma:
En
Revista:
Clin Nephrol
Ano de publicação:
2000
Tipo de documento:
Article
País de afiliação:
Japão