Chronic inflammatory demyelinating polyradiculopathy: an atypical pediatric case complicated with phrenic nerve palsy.
Turk J Pediatr
; 49(2): 210-4, 2007.
Article
em En
| MEDLINE
| ID: mdl-17907525
ABSTRACT
An atypical form of chronic inflammatory demyelinating polyneuropathy (CIDP) complicated with phrenic nerve palsy is presented with clinical and electrophysiologic features. A seven-year-old girl had initial presentation mimicking Guillain-Barré syndrome based on electrophysiologic characteristics. Between 7-11 years of age, she had five recurrences of subacute onset of weakness which usually developed over at least 2-4 months and progressed to loss of ambulation and to respiratory insufficiency. Radiologic examinations revealed unilateral phrenic nerve palsy associated with CIDP. Our patient demonstrated the rare association of CIDP and phrenic nerve palsy, resulting in diaphragmatic paralysis and respiratory failure.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Paralisia
/
Nervo Frênico
/
Polirradiculoneuropatia
/
Doenças Desmielinizantes
Tipo de estudo:
Diagnostic_studies
Limite:
Child
/
Female
/
Humans
Idioma:
En
Revista:
Turk J Pediatr
Ano de publicação:
2007
Tipo de documento:
Article
País de afiliação:
Turquia