Fenestrated sheen macular dystrophy.
Am J Ophthalmol
; 112(1): 1-7, 1991 Jul 15.
Article
em En
| MEDLINE
| ID: mdl-1882912
ABSTRACT
We examined a family with fenestrated sheen macular dystrophy. The red macular lesions were strikingly apparent in the propositus and more subtle in one affected cousin. Pronounced macular retinal pigment epithelial disruption or mottling was present in the father of the propositus, who also had markedly reduced electroretinogram rod and cone responses. The extent of electroretinogram amplitude reduction indicates abnormal function of the peripheral retina in addition to the clinically evident macular changes. Affected family members showed peripheral retinal pigment epithelial granularity. Central visual acuity remained normal despite the presence of macular lesions.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Degeneração Macular
Limite:
Adult
/
Child
/
Child, preschool
/
Female
/
Humans
/
Male
/
Middle aged
Idioma:
En
Revista:
Am J Ophthalmol
Ano de publicação:
1991
Tipo de documento:
Article