Long-term exposure of human proximal tubule cells to hydroxycobalamin[c-lactam] as a possible model to study renal disease in methylmalonic acidurias.

Sauer, S W; Opp, S; Haarmann, A; Okun, J G; Kölker, S; Morath, M A

Sauer, S W; Opp, S; Haarmann, A; Okun, J G; Kölker, S; Morath, M A.

Afiliação

Sauer SW; Department of General Pediatrics, Division of Inborn Metabolic Diseases, University Children's Hospital Heidelberg, Im Neuenheimer Feld 153, 69120, Heidelberg, Germany. Sven.Sauer@med.uni-heidelberg.de.
Opp S; Department of General Pediatrics, Division of Inborn Metabolic Diseases, University Children's Hospital Heidelberg, Im Neuenheimer Feld 153, 69120, Heidelberg, Germany.
Haarmann A; Department of General Pediatrics, Division of Inborn Metabolic Diseases, University Children's Hospital Heidelberg, Im Neuenheimer Feld 153, 69120, Heidelberg, Germany.
Okun JG; Department of General Pediatrics, Division of Inborn Metabolic Diseases, University Children's Hospital Heidelberg, Im Neuenheimer Feld 153, 69120, Heidelberg, Germany.
Kölker S; Department of General Pediatrics, Division of Inborn Metabolic Diseases, University Children's Hospital Heidelberg, Im Neuenheimer Feld 153, 69120, Heidelberg, Germany.
Morath MA; Department of General Pediatrics, Division of Inborn Metabolic Diseases, University Children's Hospital Heidelberg, Im Neuenheimer Feld 153, 69120, Heidelberg, Germany.

J Inherit Metab Dis ; 32(6): 720-727, 2009 Dec.

Article em En | MEDLINE | ID: mdl-19816787

Assuntos

Erros Inatos do Metabolismo dos Aminoácidos/patologia; Nefropatias/induzido quimicamente; Túbulos Renais Proximais/efeitos dos fármacos; Vitamina B 12/análogos & derivados; Erros Inatos do Metabolismo dos Aminoácidos/complicações; Erros Inatos do Metabolismo dos Aminoácidos/metabolismo; Animais; Células Cultivadas; Transporte de Elétrons/fisiologia; Glutationa/metabolismo; Humanos; Nefropatias/metabolismo; Nefropatias/patologia; Túbulos Renais Proximais/metabolismo; Túbulos Renais Proximais/patologia; Ácido Metilmalônico/metabolismo; Propionatos/metabolismo; Fatores de Tempo

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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Vitamina B 12 / Erros Inatos do Metabolismo dos Aminoácidos / Nefropatias / Túbulos Renais Proximais Tipo de estudo: Evaluation_studies / Prognostic_studies Limite: Animals / Humans Idioma: En Revista: J Inherit Metab Dis Ano de publicação: 2009 Tipo de documento: Article País de afiliação: Alemanha

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