Substrate Deprivation Therapy to Reduce Glycosaminoglycan Synthesis Improves Aspects of Neurological and Skeletal Pathology in MPS I Mice.

Derrick-Roberts, Ainslie L K; Jackson, Matilda R; Pyragius, Carmen E; Byers, Sharon

Derrick-Roberts, Ainslie L K; Jackson, Matilda R; Pyragius, Carmen E; Byers, Sharon.

Afiliação

Derrick-Roberts ALK; Genetics and Molecular Pathology, SA Pathology, North Adelaide, SA 5006, Australia. ainslie.derrickroberts@adelaide.edu.au.
Jackson MR; Paediatrics and Reproductive Health, The University of Adelaide, Adelaide, SA 5005, Australia. ainslie.derrickroberts@adelaide.edu.au.
Pyragius CE; Genetics and Molecular Pathology, SA Pathology, North Adelaide, SA 5006, Australia. matilda.jackson@adelaide.edu.au.
Byers S; School of Molecular & Biomedical Science, The University of Adelaide, Adelaide, SA 5005, Australia. matilda.jackson@adelaide.edu.au.

Diseases ; 5(1)2017 Feb 23.

Article em En | MEDLINE | ID: mdl-28933358

Palavras-chave

glycosaminoglycans; lysosomal storage disorder; mucopolysaccharidosis type I; rhodamine B; substrate deprivation

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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Diseases Ano de publicação: 2017 Tipo de documento: Article País de afiliação: Austrália

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