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Recurrent attacks of acute hepatic porphyria: major role of the chronic inflammatory response in the liver.
Schmitt, C; Lenglet, H; Yu, A; Delaby, C; Benecke, A; Lefebvre, T; Letteron, P; Paradis, V; Wahlin, S; Sandberg, S; Harper, P; Sardh, E; Sandvik, A K; Hov, J R; Aarsand, A K; Chiche, L; Bazille, C; Scoazec, J-Y; To-Figueras, J; Carrascal, M; Abian, J; Mirmiran, A; Karim, Z; Deybach, J-C; Puy, H; Peoc'h, K; Manceau, H; Gouya, L.
Afiliação
  • Schmitt C; Centre Français des Porphyries, Hôpital Louis Mourier, Assistance publique-Hôpitaux de Paris (AP-HP), Colombes, France.
  • Lenglet H; Centre de Recherche sur l'Inflammation (CRI), UMR1149 INSERM, Université Paris Diderot, site Bichat, Paris, France.
  • Yu A; Laboratoire d'excellence, GR-Ex, Paris, France.
  • Delaby C; Centre de Recherche sur l'Inflammation (CRI), UMR1149 INSERM, Université Paris Diderot, site Bichat, Paris, France.
  • Benecke A; Laboratoire d'excellence, GR-Ex, Paris, France.
  • Lefebvre T; STIM CNRS ERL 7368, Physiologie des Cellules Cardiaques et Vasculaires, Tours, France.
  • Letteron P; Laboratory for Clinical Biochemistry and Proteomics, Institute for Regenerative Medicine and Biotherapy (IRMB), CHU de Montpellier and Université Montpellier, Montpellier, France.
  • Paradis V; Centre National de la Recherche Scientifique, Institut des Hautes Études Scientifiques, Bures-sur-Yvette, France.
  • Wahlin S; Center for Innate Immunity and Immune Disease (CIIID), University of Washington School of Medicine, Seattle, WA, USA.
  • Sandberg S; Centre Français des Porphyries, Hôpital Louis Mourier, Assistance publique-Hôpitaux de Paris (AP-HP), Colombes, France.
  • Harper P; Centre de Recherche sur l'Inflammation (CRI), UMR1149 INSERM, Université Paris Diderot, site Bichat, Paris, France.
  • Sardh E; Laboratoire d'excellence, GR-Ex, Paris, France.
  • Sandvik AK; Centre de Recherche sur l'Inflammation (CRI), UMR1149 INSERM, Université Paris Diderot, site Bichat, Paris, France.
  • Hov JR; Centre de Recherche sur l'Inflammation (CRI), UMR1149 INSERM, Université Paris Diderot, site Bichat, Paris, France.
  • Aarsand AK; DHU Unity, Pathology Department, Hôpital Beaujon, AP-HP, Clichy, France.
  • Chiche L; Department of Gastroenterology and Hepatology, Karolinska University Hospital and Karolinska Institutet, Stockholm, Sweden.
  • Bazille C; Laboratory for Clinical Biochemistry, Norwegian Porphyria Centre (NAPOS), Haukeland University Hospital, Bergen, Norway.
  • Scoazec JY; Department of Global Health and Primary Health Care, University of Bergen, Bergen, Norway.
  • To-Figueras J; Porphyria Centre Sweden, Centre for Inherited Metabolic Diseases, Karolinska Institutet, Karolinska University Hospital, Stockholm, Sweden.
  • Carrascal M; Porphyria Centre Sweden, Centre for Inherited Metabolic Diseases, Karolinska Institutet, Karolinska University Hospital, Stockholm, Sweden.
  • Abian J; Department of Gastroenterology and Hepatology, St. Olav's University Hospital, Trondheim, Norway.
  • Mirmiran A; Department of Transplantation Medicine, Norwegian PSC Research Center and Section of Gastroenterology, Oslo University Hospital and University of Oslo, Oslo, Norway.
  • Karim Z; Laboratory for Clinical Biochemistry, Norwegian Porphyria Centre (NAPOS), Haukeland University Hospital, Bergen, Norway.
  • Deybach JC; Department of Global Health and Primary Health Care, University of Bergen, Bergen, Norway.
  • Puy H; Centre Hospitalier Universitaire Bordeaux, Chirurgie Hépatobiliaire et Pancréatique, Maison du Haut Lévèque, Bordeaux, France.
  • Peoc'h K; Service d'Anatomie Pathologique, Centre Hospitalo-Universitaire de Caen, Caen, France.
  • Manceau H; Service d'anatomopathologie, Institut Gustave Roussy, Villejuif, France.
  • Gouya L; Biochemistry and Molecular Genetics Department, Hospital Clínic, IDIBAPS, University of Barcelona, Barcelona, Spain.
J Intern Med ; 284(1): 78-91, 2018 07.
Article em En | MEDLINE | ID: mdl-29498764

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Hidroximetilbilano Sintase / Porfiria Aguda Intermitente / 5-Aminolevulinato Sintetase / Fígado Tipo de estudo: Diagnostic_studies / Etiology_studies / Incidence_studies / Observational_studies / Prevalence_studies / Prognostic_studies / Risk_factors_studies Limite: Animals / Female / Humans Idioma: En Revista: J Intern Med Assunto da revista: MEDICINA INTERNA Ano de publicação: 2018 Tipo de documento: Article País de afiliação: França

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Hidroximetilbilano Sintase / Porfiria Aguda Intermitente / 5-Aminolevulinato Sintetase / Fígado Tipo de estudo: Diagnostic_studies / Etiology_studies / Incidence_studies / Observational_studies / Prevalence_studies / Prognostic_studies / Risk_factors_studies Limite: Animals / Female / Humans Idioma: En Revista: J Intern Med Assunto da revista: MEDICINA INTERNA Ano de publicação: 2018 Tipo de documento: Article País de afiliação: França