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Mutational analysis implicates the amyloid fibril as the toxic entity in Huntington's disease.
Drombosky, Kenneth W; Rode, Sascha; Kodali, Ravi; Jacob, Tija C; Palladino, Michael J; Wetzel, Ronald.
Afiliação
  • Drombosky KW; Department of Structural Biology, University of Pittsburgh School of Medicine, Pittsburgh, PA 15260, USA; Graduate Program in Molecular Pharmacology, University of Pittsburgh School of Medicine, Pittsburgh, PA, USA; Pittsburgh Institute for Neurodegenerative Diseases (PIND), University of Pittsburgh
  • Rode S; Department of Structural Biology, University of Pittsburgh School of Medicine, Pittsburgh, PA 15260, USA; Pittsburgh Institute for Neurodegenerative Diseases (PIND), University of Pittsburgh School of Medicine, Pittsburgh, PA, USA.
  • Kodali R; Department of Structural Biology, University of Pittsburgh School of Medicine, Pittsburgh, PA 15260, USA; Pittsburgh Institute for Neurodegenerative Diseases (PIND), University of Pittsburgh School of Medicine, Pittsburgh, PA, USA.
  • Jacob TC; Department of Pharmacology & Chemical Biology, University of Pittsburgh School of Medicine, Pittsburgh, PA, USA.
  • Palladino MJ; Pittsburgh Institute for Neurodegenerative Diseases (PIND), University of Pittsburgh School of Medicine, Pittsburgh, PA, USA; Department of Pharmacology & Chemical Biology, University of Pittsburgh School of Medicine, Pittsburgh, PA, USA.
  • Wetzel R; Department of Structural Biology, University of Pittsburgh School of Medicine, Pittsburgh, PA 15260, USA; Pittsburgh Institute for Neurodegenerative Diseases (PIND), University of Pittsburgh School of Medicine, Pittsburgh, PA, USA. Electronic address: rwetzel@pitt.edu.
Neurobiol Dis ; 120: 126-138, 2018 12.
Article em En | MEDLINE | ID: mdl-30171891

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Peptídeos / Doença de Huntington / Amiloide / Mutação Limite: Animals / Humans Idioma: En Revista: Neurobiol Dis Assunto da revista: NEUROLOGIA Ano de publicação: 2018 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Peptídeos / Doença de Huntington / Amiloide / Mutação Limite: Animals / Humans Idioma: En Revista: Neurobiol Dis Assunto da revista: NEUROLOGIA Ano de publicação: 2018 Tipo de documento: Article