Multicystic Dysplastic Kidney and Incontinentia Pigmenti: Coexistence of 2 Rare Diseases.
Iran J Kidney Dis
; 13(1): 67-70, 2019 Jan.
Article
em En
| MEDLINE
| ID: mdl-30851721
ABSTRACT
Multicystic dysplastic kidney is a congenital kidney malformation consisting of multiple cysts of various sizes without a normal kidney morphology. Incontinentia pigmenti is a rare X-linked dominant genodermatosis, which is usually lethal in males, that presents clinically in 4 stages. Here, we report a case of multicystic dysplastic kidney with ureterovesical junction obstruction and incontinentia pigmenti. Coexistence of these two rare diseases may be a coincidental phenomenon or an association between the two may exist.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Incontinência Pigmentar
/
Rim Displásico Multicístico
Limite:
Child
/
Female
/
Humans
Idioma:
En
Revista:
Iran J Kidney Dis
Assunto da revista:
NEFROLOGIA
Ano de publicação:
2019
Tipo de documento:
Article
País de afiliação:
Turquia