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Management of People With a Fontan Circulation: a Cardiac Society of Australia and New Zealand Position statement.
Zentner, Dominica; Celermajer, David S; Gentles, Thomas; d'Udekem, Yves; Ayer, Julian; Blue, Gillian M; Bridgman, Cameron; Burchill, Luke; Cheung, Michael; Cordina, Rachael; Culnane, Evelyn; Davis, Andrew; du Plessis, Karin; Eagleson, Karen; Finucane, Kirsten; Frank, Belinda; Greenway, Sebastian; Grigg, Leeanne; Hardikar, Winita; Hornung, Tim; Hynson, Jenny; Iyengar, Ajay J; James, Paul; Justo, Robert; Kalman, Jonathan; Kasparian, Nadine; Le, Brian; Marshall, Kate; Mathew, Jacob; McGiffin, David; McGuire, Mark; Monagle, Paul; Moore, Ben; Neilsen, Julie; O'Connor, Bernadette; O'Donnell, Clare; Pflaumer, Andreas; Rice, Kathryn; Sholler, Gary; Skinner, Jonathan R; Sood, Siddharth; Ward, Juliet; Weintraub, Robert; Wilson, Tom; Wilson, William; Winlaw, David; Wood, Angela.
Afiliação
  • Zentner D; Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Genomic Medicine, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Medicine, University of Melbourne, Melbourne, Vic, Austr
  • Celermajer DS; Department of Cardiology, Royal Prince Alfred Hospital, Sydney, NSW, Australia; Faculty of Medicine and Health, University of Sydney, Sydney, NSW, Australia.
  • Gentles T; Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.
  • d'Udekem Y; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Cardiac Surgery, Royal Children's Hospital, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia.
  • Ayer J; Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.
  • Blue GM; Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.
  • Bridgman C; Department of Cardiology, Flinders Medical Centre, Adelaide, SA, Australia.
  • Burchill L; Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia.
  • Cheung M; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia.
  • Cordina R; Department of Cardiology, Royal Prince Alfred Hospital, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.
  • Culnane E; Transition Support Service, Royal Children's Hospital, Melbourne, Vic, Australia.
  • Davis A; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia.
  • du Plessis K; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia.
  • Eagleson K; Faculty of Medicine, University of Queensland, Brisbane, Qld, Australia; Queensland Paediatric Cardiac Research, Children's Health Queensland, Brisbane, Qld, Australia.
  • Finucane K; Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.
  • Frank B; Australian and New Zealand Fontan Advocacy Committee, Australia and New Zealand.
  • Greenway S; Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.
  • Grigg L; Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia.
  • Hardikar W; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Gastroenterology and Clinical Nutrition, Royal Children's Hospital, Melbourne, Vic, Australia.
  • Hornung T; Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.
  • Hynson J; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Victorian Paediatric Palliative Care Program, Royal Children's Hospital, Melbourne, Vic, Australia.
  • Iyengar AJ; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Cardiac Surgery, Royal Children's Hospital, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia.
  • James P; Department of Genomic Medicine, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Pathology, University of Melbourne, Melbourne, Vic, Australia.
  • Justo R; Faculty of Medicine, University of Queensland, Brisbane, Qld, Australia; Queensland Paediatric Cardiac Research, Children's Health Queensland, Brisbane, Qld, Australia.
  • Kalman J; Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia.
  • Kasparian N; Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia; Discipline of Paediatrics, School of Women's and Children's Health, UNSW Medicine, University of New South Wales, Sydney, NSW, Australia.
  • Le B; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia; Palliative Care, Royal Melbourne Hospital, Melbourne, Vic, Australia.
  • Marshall K; Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia; Discipline of Paediatrics, School of Women's and Children's Health, UNSW Medicine, University of New South Wales, Sydney, NSW, Australia.
  • Mathew J; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia.
  • McGiffin D; Department of Cardiothoracic Surgery, Alfred Health, Melbourne, Vic, Australia; Department of Surgery, Monash University, Melbourne, Vic, Australia.
  • McGuire M; Department of Cardiology, Royal Prince Alfred Hospital, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.
  • Monagle P; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Haematology, Royal Children's Hospital, Melbourne, Vic, Australia.
  • Moore B; Department of Cardiology, Royal Prince Alfred Hospital, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.
  • Neilsen J; Heart Kids NZ, Auckland, New Zealand.
  • O'Connor B; llied Health, Royal Children's Hospital, Melbourne, Vic, Australia.
  • O'Donnell C; Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.
  • Pflaumer A; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia.
  • Rice K; Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.
  • Sholler G; Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.
  • Skinner JR; Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.
  • Sood S; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia; Department of Gastroenterology and Hepatology, Royal Melbourne Hospital, Melbourne, Vic, Australia.
  • Ward J; Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia.
  • Weintraub R; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia.
  • Wilson T; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia.
  • Wilson W; Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia.
  • Winlaw D; Faculty of Medicine and Health, University of Sydney, Sydney, NSW, Australia; Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia.
  • Wood A; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia; ongenital Heart Alliance of Australia and New Zealand Registry Board, Melbourne, Vic, Australia.
Heart Lung Circ ; 29(1): 5-39, 2020 Jan.
Article em En | MEDLINE | ID: mdl-31735685
ABSTRACT
The Fontan circulation describes the circulatory state resulting from an operation in congenital heart disease where systemic venous return is directed to the lungs without an intervening active pumping chamber. As survival increases, so too does recognition of the potential health challenges. This document aims to allow clinicians, people with a Fontan circulation, and their families to benefit from consensus agreement about management of the person with a Fontan circulation. The document was crafted with input from a multidisciplinary group of health care providers as well as individuals with a Fontan circulation and families. It is hoped that the shared common vision of long-term wellbeing will continue to drive improvements in care and quality of life in this patient population and eventually translate into improved survival. KEYPOINTS.
Assuntos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Sistema de Registros / Cardiopatias Congênitas Limite: Humans País/Região como assunto: Oceania Idioma: En Revista: Heart Lung Circ Assunto da revista: ANGIOLOGIA / CARDIOLOGIA Ano de publicação: 2020 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Sistema de Registros / Cardiopatias Congênitas Limite: Humans País/Região como assunto: Oceania Idioma: En Revista: Heart Lung Circ Assunto da revista: ANGIOLOGIA / CARDIOLOGIA Ano de publicação: 2020 Tipo de documento: Article