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Mechanistic understanding of the combined immunodeficiency in complete human CARD11 deficiency.
Lu, Henry Y; Sharma, Mehul; Sharma, Ashish A; Lacson, Atilano; Szpurko, Ashley; Luider, Joanne; Dharmani-Khan, Poonam; Shameli, Afshin; Bell, Peter A; Guilcher, Gregory M T; Lewis, Victor A; Vasquez, Marta Rojas; Desai, Sunil; McGonigle, Lyle; Murguia-Favela, Luis; Wright, Nicola A M; Sergi, Consolato; Wine, Eytan; Overall, Christopher M; Suresh, Sneha; Turvey, Stuart E.
Afiliação
  • Lu HY; Department of Pediatrics, British Columbia Children's Hospital, The University of British Columbia, Vancouver, British Columbia, Canada; Experimental Medicine Program, Faculty of Medicine, The University of British Columbia, Vancouver, British Columbia, Canada.
  • Sharma M; Department of Pediatrics, British Columbia Children's Hospital, The University of British Columbia, Vancouver, British Columbia, Canada; Experimental Medicine Program, Faculty of Medicine, The University of British Columbia, Vancouver, British Columbia, Canada.
  • Sharma AA; Department of Pathology, Case Western Reserve University, Cleveland, Ohio; Department of Pathology, Emory University, Atlanta, Ga.
  • Lacson A; Department of Laboratory Medicine and Pathology, University of Alberta, Edmonton, Alberta, Canada.
  • Szpurko A; Section of Oncology/Bone Marrow Therapy, Departments of Oncology and Pediatrics, Alberta Children's Hospital, University of Calgary, Calgary, Alberta, Canada.
  • Luider J; Department of Pathology and Laboratory Medicine, University of Calgary, Alberta Precision Laboratories, Calgary, Alberta, Canada.
  • Dharmani-Khan P; Department of Pathology and Laboratory Medicine, University of Calgary, Alberta Precision Laboratories, Calgary, Alberta, Canada.
  • Shameli A; Department of Pathology and Laboratory Medicine, University of Calgary, Alberta Precision Laboratories, Calgary, Alberta, Canada.
  • Bell PA; Centre for Blood Research, The University of British Columbia, Vancouver, British Columbia, Canada; Department of Oral Biological and Medical Sciences, Faculty of Dentistry, The University of British Columbia, Vancouver, British Columbia, Canada.
  • Guilcher GMT; Section of Oncology/Bone Marrow Therapy, Departments of Oncology and Pediatrics, Alberta Children's Hospital, University of Calgary, Calgary, Alberta, Canada.
  • Lewis VA; Section of Oncology/Bone Marrow Therapy, Departments of Oncology and Pediatrics, Alberta Children's Hospital, University of Calgary, Calgary, Alberta, Canada.
  • Vasquez MR; Department of Pediatrics, Division of Immunology, Hematology, Oncology and Palliative Care (iHOPE), University of Alberta, Edmonton, Alberta, Canada.
  • Desai S; Department of Pediatrics, Division of Immunology, Hematology, Oncology and Palliative Care (iHOPE), University of Alberta, Edmonton, Alberta, Canada.
  • McGonigle L; Department of Pediatrics, Division of General and Community Pediatrics, University of Alberta, Edmonton, Alberta, Canada.
  • Murguia-Favela L; Section of Pediatric Hematology-Immunology, Department of Pediatrics, Alberta Children's Hospital, University of Calgary, Calgary, Alberta, Canada.
  • Wright NAM; Section of Pediatric Hematology-Immunology, Department of Pediatrics, Alberta Children's Hospital, University of Calgary, Calgary, Alberta, Canada.
  • Sergi C; Department of Laboratory Medicine and Pathology, University of Alberta, Edmonton, Alberta, Canada.
  • Wine E; Division of Pediatric Gastroenterology and Nutrition, Department of Pediatrics, University of Alberta, Edmonton, Alberta, Canada.
  • Overall CM; Centre for Blood Research, The University of British Columbia, Vancouver, British Columbia, Canada; Department of Oral Biological and Medical Sciences, Faculty of Dentistry, The University of British Columbia, Vancouver, British Columbia, Canada.
  • Suresh S; Department of Pediatrics, Division of Immunology, Hematology, Oncology and Palliative Care (iHOPE), University of Alberta, Edmonton, Alberta, Canada.
  • Turvey SE; Department of Pediatrics, British Columbia Children's Hospital, The University of British Columbia, Vancouver, British Columbia, Canada; Experimental Medicine Program, Faculty of Medicine, The University of British Columbia, Vancouver, British Columbia, Canada. Electronic address: sturvey@cw.bc.ca.
J Allergy Clin Immunol ; 148(6): 1559-1574.e13, 2021 12.
Article em En | MEDLINE | ID: mdl-33872653

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Linfócitos T Auxiliares-Indutores / Transplante de Células-Tronco Hematopoéticas / Centro Germinativo / Proteínas Adaptadoras de Sinalização CARD / Células Precursoras de Linfócitos B / Doenças da Imunodeficiência Primária / Guanilato Ciclase / Mutação Limite: Adolescent / Child / Humans / Infant / Male Idioma: En Revista: J Allergy Clin Immunol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Canadá

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Linfócitos T Auxiliares-Indutores / Transplante de Células-Tronco Hematopoéticas / Centro Germinativo / Proteínas Adaptadoras de Sinalização CARD / Células Precursoras de Linfócitos B / Doenças da Imunodeficiência Primária / Guanilato Ciclase / Mutação Limite: Adolescent / Child / Humans / Infant / Male Idioma: En Revista: J Allergy Clin Immunol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Canadá