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Modulation of mitochondrial and inflammatory homeostasis through RIP140 is neuroprotective in an adrenoleukodystrophy mouse model.
Ranea-Robles, Pablo; Galino, Jorge; Espinosa, Lluís; Schlüter, Agatha; Ruiz, Montserrat; Calingasan, Noel Ylagan; Villarroya, Francesc; Naudí, Alba; Pamplona, Reinald; Ferrer, Isidre; Beal, M Flint; Portero-Otín, Manuel; Fourcade, Stéphane; Pujol, Aurora.
Afiliação
  • Ranea-Robles P; Neurometabolic Diseases Laboratory, Bellvitge Biomedical Research Institute (IDIBELL), Barcelona, Spain.
  • Galino J; CIBERER U759, Center for Biomedical Research on Rare Diseases, ISCIII, Madrid, Spain.
  • Espinosa L; Department of Genetics and Genomic Sciences, Icahn Institute for Data Science and Genomic Technology, Icahn School of Medicine at Mount Sinai, New York, New York, USA.
  • Schlüter A; Neurometabolic Diseases Laboratory, Bellvitge Biomedical Research Institute (IDIBELL), Barcelona, Spain.
  • Ruiz M; CIBERER U759, Center for Biomedical Research on Rare Diseases, ISCIII, Madrid, Spain.
  • Calingasan NY; Institut Municipal d'Investigacions Mèdiques, Hospital del Mar, Barcelona, Spain.
  • Villarroya F; Neurometabolic Diseases Laboratory, Bellvitge Biomedical Research Institute (IDIBELL), Barcelona, Spain.
  • Naudí A; CIBERER U759, Center for Biomedical Research on Rare Diseases, ISCIII, Madrid, Spain.
  • Pamplona R; Neurometabolic Diseases Laboratory, Bellvitge Biomedical Research Institute (IDIBELL), Barcelona, Spain.
  • Ferrer I; CIBERER U759, Center for Biomedical Research on Rare Diseases, ISCIII, Madrid, Spain.
  • Beal MF; Feil Family Brain and Mind Research Institute, Weill Cornell Medical College, New York, New York, USA.
  • Portero-Otín M; Department of Biochemistry and Molecular Biomedicine and Institut de Biomedicina, University of Barcelona, Barcelona, Catalonia, Spain.
  • Fourcade S; Fisiopatología de la Obesidad y Nutrición, CIBER, Madrid, Spain.
  • Pujol A; Experimental Medicine Department, University of Lleida-IRBLleida, Lleida, Spain.
Neuropathol Appl Neurobiol ; 48(1): e12747, 2022 02.
Article em En | MEDLINE | ID: mdl-34237158

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Adrenoleucodistrofia Tipo de estudo: Prognostic_studies Limite: Animals Idioma: En Revista: Neuropathol Appl Neurobiol Ano de publicação: 2022 Tipo de documento: Article País de afiliação: Espanha

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Adrenoleucodistrofia Tipo de estudo: Prognostic_studies Limite: Animals Idioma: En Revista: Neuropathol Appl Neurobiol Ano de publicação: 2022 Tipo de documento: Article País de afiliação: Espanha