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Severe adult hemophagocytic lymphohistiocytosis (HLHa) correlates with HLH-related gene variants.
Bloch, Coralie; Jais, Jean Philippe; Gil, Marine; Boubaya, Marouane; Lepelletier, Yves; Bader-Meunier, Brigitte; Mahlaoui, Nizar; Garcelon, Nicolas; Lambotte, Olivier; Launay, David; Larroche, Claire; Lazaro, Estibaliz; Liffermann, Francois; Lortholary, Olivier; Michel, Marc; Michot, Jean-Marie; Morel, Pierre; Cheminant, Morgane; Suarez, Felipe; Terriou, Louis; Urbanski, Geoffrey; Viallard, Jean-Francois; Alcais, Alexandre; Fischer, Alain; de Saint Basile, Geneviève; Hermine, Olivier.
Afiliação
  • Bloch C; Clinical Research Unit, Avicenne University Hospital, AP-HP, Bobigny, France; Paris 13 University, Sorbonne Paris Cité, Paris, France; Laboratory of Cellular and Molecular Mechanisms of Hematological Disorders and Therapeutical Implications, INSERM UMR1163/CNRS URL 8254, Paris, France; French Nation
  • Jais JP; Imagine Institute, Université Paris Cité, Paris, France; Biostatistic Unit, Necker University Hospital, AP-HP, Paris, France; Human Genetics of Infectious Diseases: Complex Predisposition, INSERM UMR1163, Paris, France.
  • Gil M; Imagine Institute, Université Paris Cité, Paris, France.
  • Boubaya M; Clinical Research Unit, Avicenne University Hospital, AP-HP, Bobigny, France.
  • Lepelletier Y; Laboratory of Cellular and Molecular Mechanisms of Hematological Disorders and Therapeutical Implications, INSERM UMR1163/CNRS URL 8254, Paris, France; Imagine Institute, Université Paris Cité, Paris, France.
  • Bader-Meunier B; Imagine Institute, Université Paris Cité, Paris, France; Department of Pediatric Immunology and Rheumatology, Necker University Hospital, AP-HP, Paris, France.
  • Mahlaoui N; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France; Department of Pediatric Immunology and Rheumatology, Necker University Hospital, AP-HP, Paris, France.
  • Garcelon N; Imagine Institute, Université Paris Cité, Paris, France.
  • Lambotte O; University Paris Saclay, AP-HP, Hôpital Bicêtre, IMVAHB UMR1184, INSERM, CEA, Le Kremlin Bicêtre, France.
  • Launay D; Université de Lille, CHU Lille, Département de Médecine Interne et Immunologie Clinique, Centre de Référence des Maladies Auto-immunes Systémiques Rares du Nord et Nord-Ouest de France, Lille, France; INSERM INFINITE U1286, Lille, France.
  • Larroche C; Internal Medicine Unit, Avicenne Hospital, AP-HP, Bobigny, France.
  • Lazaro E; Internal Medicine Department, Bordeaux Hospital University, Bordeaux, France; CNRS-UMR 5164 Immuno ConcEpT, Bordeaux, France.
  • Liffermann F; Service de medecine interne-hematologie, Centre hospitalier de Dax, Dax, France.
  • Lortholary O; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France; Service de Maladies Infectieuses et Tropicales, Centre d'Infectiologie Necker Pasteur, Hôpital Universitaire Necker-Enfants Malades, Assis
  • Michel M; Department of Internal Medicine, Centre de Référence maladies rares sur les Cytopénies Auto-Immunes de l'adulte, Hôpitaux Universitaires Henri Mondor, AP-HP, Université Paris-Est Créteil, Créteil, France.
  • Michot JM; Gustave Roussy, University Paris Saclay, Drug Development Department, Villejuif, France.
  • Morel P; Service d'Hématologie Clinique, Hôpital Schaffner de Lens, Lens Cedex, France.
  • Cheminant M; Laboratory of Cellular and Molecular Mechanisms of Hematological Disorders and Therapeutical Implications, INSERM UMR1163/CNRS URL 8254, Paris, France; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, P
  • Suarez F; Laboratory of Cellular and Molecular Mechanisms of Hematological Disorders and Therapeutical Implications, INSERM UMR1163/CNRS URL 8254, Paris, France; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, P
  • Terriou L; Université de Lille, CHU Lille, Département de Médecine Interne et Immunologie Clinique, Centre de Référence des Maladies Auto-immunes Systémiques Rares du Nord et Nord-Ouest de France, Lille, France; INSERM INFINITE U1286, Lille, France.
  • Urbanski G; Department of Internal Medicine and Clinical Immunology, University Hospital, Angers, France; MitoLab Team, MITOVASC Institute, UMR CNRS 6015, INSERM U1083, University of Angers, Angers, France.
  • Viallard JF; Internal Medicine Department, Bordeaux Hospital University, Bordeaux, France.
  • Alcais A; Imagine Institute, Université Paris Cité, Paris, France; Biostatistic Unit, Necker University Hospital, AP-HP, Paris, France; Human Genetics of Infectious Diseases: Complex Predisposition, INSERM UMR1163, Paris, France.
  • Fischer A; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France; Department of Pediatric Immunology and Rheumatology, Necker University Hospital, AP-HP, Paris, France; Laboratory of Normal and Pathologic
  • de Saint Basile G; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, Paris, France; Laboratory of Normal and Pathological Homeostasis of the Immune System, INSERM UMR1163, Paris, France.
  • Hermine O; Laboratory of Cellular and Molecular Mechanisms of Hematological Disorders and Therapeutical Implications, INSERM UMR1163/CNRS URL 8254, Paris, France; French National Center for Primary Immunodeficiencies, Necker University Hospital, AP-HP, Paris, France; Imagine Institute, Université Paris Cité, P
J Allergy Clin Immunol ; 153(1): 256-264, 2024 01.
Article em En | MEDLINE | ID: mdl-37678575

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Linfo-Histiocitose Hemofagocítica Tipo de estudo: Prognostic_studies Limite: Adolescent / Adult / Humans Idioma: En Revista: J Allergy Clin Immunol Ano de publicação: 2024 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Linfo-Histiocitose Hemofagocítica Tipo de estudo: Prognostic_studies Limite: Adolescent / Adult / Humans Idioma: En Revista: J Allergy Clin Immunol Ano de publicação: 2024 Tipo de documento: Article