Endovascular closure of a congenital extrahepatic portosystemic shunt for the treatment of hepatopulmonary syndrome in an infant.
Pediatr Radiol
; 54(2): 357-361, 2024 02.
Article
em En
| MEDLINE
| ID: mdl-38141079
ABSTRACT
Congenital portosystemic shunts may result in the development of hepatopulmonary syndrome, typically presenting with progressive hypoxemia in later childhood. We describe a case of a 5-month-old male with heterotaxy with polysplenia presenting with new onset hypoxemia. Subsequent evaluation identified an extrahepatic portosystemic shunt arising from the confluence of the main portal and superior mesenteric veins draining into the left renal vein. To treat his hypoxemia and prevent future complications of shunting, the patient underwent a successful single-stage endovascular closure.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Derivação Portossistêmica Transjugular Intra-Hepática
/
Síndrome Hepatopulmonar
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Malformações Vasculares
Limite:
Child
/
Humans
/
Infant
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Male
Idioma:
En
Revista:
Pediatr Radiol
Ano de publicação:
2024
Tipo de documento:
Article
País de afiliação:
Estados Unidos