RESUMEN
Cutaneous amyloidosis is a rare disease characterized by the deposition of amyloid in the dermis. It can be primary or secondary, depending on associated diseases. It has been linked to various autoimmune diseases, including primary biliary cirrhosis. We present the case of a patient with an autoimmune hepatitis-primary biliary cirrhosis overlap syndrome with concomitant cutaneous amyloidosis, a very unusual association, and discuss similar cases and possible pathophysiological implications.
Asunto(s)
Amiloidosis Familiar/etiología , Autoinmunidad , Hepatitis Autoinmune/complicaciones , Cirrosis Hepática Biliar/complicaciones , Enfermedades Cutáneas Genéticas/etiología , Adulto , Amiloidosis Familiar/diagnóstico , Amiloidosis Familiar/inmunología , Biopsia , Diagnóstico Diferencial , Hepatitis Autoinmune/diagnóstico , Hepatitis Autoinmune/inmunología , Humanos , Hígado/patología , Cirrosis Hepática Biliar/diagnóstico , Cirrosis Hepática Biliar/inmunología , Masculino , Piel/patología , Enfermedades Cutáneas Genéticas/diagnóstico , Enfermedades Cutáneas Genéticas/inmunología , SíndromeRESUMEN
BACKGROUND: Dermatology patients are mostly seen in outpatient clinics; however, there is a significant need for consultations within the hospital setting. METHODS: Here we describe the hospital consultations received by the Dermatology Service during a 3-year period. RESULTS: Most of the requested consultations came from the Internal Medicine Department and the surgical departments. The most common encountered dermatoses were drug eruptions and adnexal diseases, followed by viral dermatoses. CONCLUSIONS: In hospital dermatology may pose a challenge for other clinicians; therefore, dermatologists should be adequately trained to confront a wide variety of clinical scenarios.