Extensive Melanotic Neuroectodermal Tumor of Infancy.

The melanotic neuroectodermal tumor of infancy (MNTI) is a rare childhood neoplasm with an alarming but classical clinical presentation. We present the case of a 2-month-old male infant treated with surgery for an aggressive MNTI on the alveolar process of the maxilla. Radiographic examination showed a diffuse osteolytic radiolucent lesion in the right maxilla, and displacement and dysmorphic changes in the developing primary tooth buds. The patient remained well without evidence of recurrence for 6 months after surgery. We discussed clinicopathological features, management alternatives, and outcome.

Plasmacytoid Myoepithelioma of the Hard Palate in a Child - A Rare Case Report.

Myoepithelioma is a rare tumour accounting for 1-1.5% of salivary gland tumours, 21% of which occur in soft & hard palate. Cytologic features of these tumours are not well established leading to diagnostic pitfall in many cases on FNAC. However, as radiologic findings are overlapping and inconclusive in salivary gland tumours, preoperative cytologic diagnosis may help surgeons to plan surgery especially in patients requiring facial surgery. Here, we present a rare case of plasmacytoid myoepithelioma of the hard palate in an 11-year-old boy which was conclusively diagnosed on FNAC and further confirmed by histopathological and immunohistochemical studies. We have made an attempt to describe cytologic features of myoepithelioma with differential diagnosis of these tumours through review of literature.