Basal cell nevus syndrome concurrent with adenoid cystic carcinoma of salivary gland.
J Am Acad Dermatol
; 48(5 Suppl): S64-6, 2003 May.
Article
en En
| MEDLINE
| ID: mdl-12734479
ABSTRACT
Basal cell nevus syndrome is a genetically determined disease characterized by 5 major manifestations (multiple basal cell carcinomas, jaw cysts, skeletal abnormalities, pits of the hands and feet, and ectopic calcification) and a variety of developmental anomalies. We present a case of basal cell nevus syndrome in which the patient had adenoid cystic carcinoma of the minor salivary glands develop in the soft palate resulting in distant pulmonary metastases. The patient died at the age of 44 years of respiratory complications. To our knowledge, this is the first simultaneous occurrence of basal cell nevus syndrome with adenoid cystic carcinoma of salivary gland.
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Bases de datos:
MEDLINE
Asunto principal:
Neoplasias de las Glándulas Salivales
/
Síndrome del Nevo Basocelular
/
Carcinoma Adenoide Quístico
/
Metástasis Linfática
Límite:
Adult
/
Humans
/
Male
Idioma:
En
Revista:
J Am Acad Dermatol
Año:
2003
Tipo del documento:
Article
País de afiliación:
Turquía