A case of idiopathic sclerosing mediastinitis in a 7-year-old Japanese boy.
Eur J Pediatr
; 164(5): 302-5, 2005 May.
Article
en En
| MEDLINE
| ID: mdl-15726406
ABSTRACT
UNLABELLED Sclerosing mediastinitis is a very rare benign disorder characterised by the development of dense fibrous tissue within the mediastinum. Affected patients are typically young adults with infant cases being uncommon especially in areas without endemic histoplasmosis. We report a Japanese boy with markedly elevated serum inflammatory markers for more than 1 year in the absence of any clinical manifestations. 67Ga-scintigraphy demonstrated an accumulation in the mediastinal region and an open biopsy revealed a hard fibrous mass in the anteriosuperior mediastinum. Thus, a diagnosis of idiopathic sclerosing mediastinitis was made. CONCLUSION:
To the best of our knowledge, this case is the youngest patient reported with this disorder. In patients with mediastinal mass lesions the diagnosis of sclerosing mediastinitis should be considered as well as infectious, autoimmune or neoplastic disease even in children.
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Bases de datos:
MEDLINE
Asunto principal:
Mediastinitis
/
Mediastino
Tipo de estudio:
Etiology_studies
Límite:
Child
/
Humans
/
Male
País/Región como asunto:
Asia
Idioma:
En
Revista:
Eur J Pediatr
Año:
2005
Tipo del documento:
Article
País de afiliación:
Japón