Hemophagocytic Lymphohistiocytosis in a Newborn Presenting as "Blueberry Muffin Baby".
Pediatr Dermatol
; 34(3): e150-e151, 2017 May.
Article
en En
| MEDLINE
| ID: mdl-28523896
ABSTRACT
Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening hyperinflammatory syndrome characterized by uncontrolled activation and proliferation of proinflammatory cytokines. Initial presentation commonly includes fever, hepatosplenomegaly, and pancytopenia; 6 to 65% of cases also have a concurrent cutaneous eruption. We present the case of a 6-day-old premature infant boy with congenital severe thrombocytopenia, anemia, and hepatosplenomegaly who presented with several cutaneous violaceous papules and nodules and was found to have HLH.
Texto completo:
1
Bases de datos:
MEDLINE
Asunto principal:
Recien Nacido Prematuro
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Linfohistiocitosis Hemofagocítica
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Exantema
Tipo de estudio:
Diagnostic_studies
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Etiology_studies
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Observational_studies
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Prognostic_studies
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Risk_factors_studies
Límite:
Humans
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Male
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Newborn
Idioma:
En
Revista:
Pediatr Dermatol
Año:
2017
Tipo del documento:
Article